Hepatic angiomyolipoma (AML) is notoriously difficult to diagnose without an invasive surgery even with the recent development of the various imaging modalities. Additionally, recent reports showed its malignant behavior after the surgery; it is important to diagnose the character of each tumor including the possible malignant potential and determine the postoperative management for each case. ...

OBJECTIVE To assess the importance of management and close follow-up of patients with tuberous sclerosis that associate renal angiomyolipomas. METHODS To report a case. RESULTS A 55 years old men with tuberous sclerosis diagnosed in childhood and later finding of bilateral giant renal masses in imaging studies, with significant compromise of renal function. The patient did not have a proper...

A thirty-three-year-old white male was admitted for evaluation of pain in the right flank of four days’ duration, unassociated with fever, dysuria, or hematuria. Past medical history was negative for calculous disease or trauma. The diagnosis of tuberous sclerosis had been made previously for which seizure activity was controlled with diphenylhydantoin and phenobarbital. Findings on physical ex...

Perivascular Epithelioid Cell Tumors (PEComas) are a family of rare neoplasms defined as mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells [1]. Pea et al. first noted this unusual cell type in both renal angiomyolipoma (AML) and clear-cell “sugar” tumor (CCST) of the lung [2]. This generated the concept of a family of neoplasms co...

A 47-year-old woman was referred to our hospital for the management of her large abdominal mass. She had a history of right flank pain off and on for 2-3 years. She was admitted to the provincial hospital in the previous four days due to right flank pain and nausea. She had no history of trauma. Abdominal computed tomography (CT) was performed and liposarcoma was suspected in the right flank. S...