Multiple bilateral pulmonary arterio-venous malformations (PAVM) were diagnosed in a 15-year-old girl with erythrocytosis. Although transcatheter embolotherapy is generally accepted as a treatment of PAVM, the largest lesion in the right lower lobe was fed by a 13-mm diameter feeding artery without downstream narrowing, which was unsafe for the embolization of coils or balloons. Instead, we sur...

Pulmonary arteriovenous fistulas (PAVFs) are rare vascular malformations (PAVMs) of the lung that could lead to severe hypoxiemia due to right-to-left intrapulmonary shunts. They may occur as isolated entities or associated with Osler-Rendu-Weber syndrome or hereditary haemorrhagic telangiectasia (HHT). We study 3 patients with Rendu-OslerWeber disease and a large arteriovenous malformation inv...

A 3-year-old Chinese boy was diagnosed with ipsilateral congenital malformations: right lung hypoplasia, dextroversion of heart, atrial septal defect, hepatic vein drainage directly into the right atrium, facial asymmetry, right microtia and congenital deafness, and indirect inguinal hernia. He underwent indirect inguinal hernia repair at the age of 2. Although without any facial plastic surger...

Proteus syndrome is a complex disorder consisting variably of disproportionate, asymmetric overgrowth of body parts; cerebriform connective tissue nevi; epidermal nevi; vascular malformations of the capillary, venous, and lymphatic types; and dysregulated adipose tissue. Serious complications may ensue, such as pulmonary embolism, cystic lung disease, and various neoplasms. Somatic mosaicism, l...

many studies have shown that mycotoxin contamination of agricultural products is a challenge for individual's health espe­cially in developing countries. improper production and storage of foods, prepare conditions for aflatoxin production in crops, especially rice, wheat, pistachio, walnut, almond, etc which are the main sources of foods for people. feeding live­stock by contaminated bread is ...

abstract background: the gamma knife radiosurgery (gkr) is an established management option for cerebral ar-teriovenous malformations (avms). therapeutic benefits of radiosurgery for arteriovenous malformations are complete obliteration of nidus with minimal neurological deficit. methods: radiosurgery was performed between february 2003 and april 2010 at kamraniye day clinic, teh-ran, iran, usi...

Pulmonary sequestration refers to lack of normal airway connection and aberrant vascular supply, and it may be either intralobar or extralobar. Bronchial atresia involving the lower lobes, especially the left lower lobe, is often associated with aberrant systemic arterial connection, forming an “intralobar sequestration” in which a region of parenchyma is functionally isolated from the remainde...

Pulmonary vascular malformation is an unusual cause of hemoptysis. These abnormal vascular communications between pulmonary circulations or between pulmonary and systemic circulations can result in significant dyspnea, hemoptysis and hypoxemia. Pulmonary vascular malformations can take various forms. Here we present a case of an abnormal collection of thrombosed arteries and veins, without the ...

In this review, the role of wall shear stress in the chicken embryonic heart is analyzed to determine its effect on cardiac development through regulating gene expression. Therefore, background information is provided for fluid dynamics, normal chicken and human heart development, cardiac malformations, cardiac and vitelline blood flow, and a chicken model to induce cardiovascular anomalies. A ...

Congenital cystic adenomatoid malformation, currently referred as congenital pulmonary airway malformation (CPAM), is one of the rare lung malformations seen in adults. We report a case of a 59-year-old male with a chronic cough and hemoptysis that was not amenable to bronchial embolization. Further work up revealed cystic changes with fungal ball and type 1 CPAM. Patients with this condition w...