نتایج جستجو برای: fanconi bickel syndrome

تعداد نتایج: 624826  

Journal: :Oncology letters 2017
Yong Lin Fan Pan Yingchao Wang Ziqian Chen Chun Lin Lvfeng Yao Xin Zhang Rui Zhou Chen Pan

The aim of the present study was to identify monitoring and prevention measures as well as predictive factors for early detection of renal toxicity associated with long-term administration of adefovir dipivoxil in order to avoid progression to Fanconi syndrome. Clinical data of 28 patients with Fanconi syndrome caused by long-term administration of adefovir dipivoxil for the treatment of chroni...

Journal: :Journal of the American Society of Nephrology : JASN 2014
Héloïse P Gaide Chevronnay Virginie Janssens Patrick Van Der Smissen Francisca N'Kuli Nathalie Nevo Yves Guiot Elena Levtchenko Etienne Marbaix Christophe E Pierreux Stéphanie Cherqui Corinne Antignac Pierre J Courtoy

Cystinosis, a main cause of Fanconi syndrome, is reproduced in congenic C57BL/6 cystinosin knockout (KO) mice. To identify the sequence of pathogenic and adaptation mechanisms of nephropathic cystinosis, we defined the onset of Fanconi syndrome in KO mice between 3 and 6 months of age and analyzed the correlation with structural and functional changes in proximal tubular cells (PTCs), with focu...

2013
W. B. Rizzo G. S. Harper

11 children with either cystinosis or Lowe's syndrome had a reduced content of plasma and muscle carnitine due to renal Fanconi syndrome. After treatment with oral L-carnitine, 100 mg/kg per d divided every 6 h, plasma carnitine concentrations became normal in all subjects within 2 d. Initial plasma free fatty acid concentrations, inversely related to free carnitine concentrations, were reduced...

Journal: :International Journal of Contemporary Pediatrics 2018

Journal: :Journal of Veterinary Internal Medicine 2017

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