نتایج جستجو برای: fabry disease

تعداد نتایج: 1493456  

2015
Hee Seung Lee Shawn Betts John R. Anderson

Title Page Title: How can we design effective instructions to promote transfer? Author(s): Hee Seung Lee, Shawn Betts, and John R. Anderson Hee Seung Lee Carnegie Mellon University [email protected] Shawn Betts Carnegie Mellon University [email protected] John R. Anderson Carnegie Mellon University [email protected]

Journal: :Clinical chemistry 2005
Maria Fuller Peter C Sharp Tina Rozaklis Phillip D Whitfield David Blacklock John J Hopwood Peter J Meikle

BACKGROUND Fabry disease is an X-linked lysosomal storage disorder resulting from a deficiency of the lysosomal hydrolase, alpha-galactosidase, for which enzyme replacement therapy is now available. In this study, we aimed to identify Fabry heterozygotes not only for genetic counseling of families but because it is becoming increasingly obvious that many heterozygous (carrier) females are sympt...

Journal: :Best Practice & Research Clinical Endocrinology & Metabolism 2015

Journal: :Journal of Inborn Errors of Metabolism and Screening 2014

Journal: :American Journal of Hypertension 2004

Journal: :Stroke Research and Treatment 2011

Journal: :Journal of Inborn Errors of Metabolism and Screening 2016

Journal: :Postgraduate Medical Journal 2018

Journal: :Journal of the American College of Cardiology 2021

Fabry disease (FD) is a rare X-linked inherited lysosomal storage disorder caused by deficient α-galactosidase A activity that leads to an accumulation of globotriasylceramide (Gb3) in affected tissues, including the heart. Cardiovascular involvement usually manifests as left ventricular hypertrophy, myocardial fibrosis, heart failure, and arrhythmias, which limit quality life represent most co...

Journal: :Reviews in Cardiovascular Medicine 2022

Echocardiography is the most common diagnostic tool to screen for Fabry cardiomyopathy as it fast, non-invasive, low-cost, widely available, easily applicable and reproducible. first-line investigation, being useful in all stages of disease: (1) gene-positive patients, unveil signs early cardiac involvement allowing timely treatment; (2) patients with overt estimate severity involvement, possib...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید