Figure 1. Preoperative photograph showing the overlying melanocytic nevi. DESCRIPTION We present a 13-year-old male patient with congenital melanocytic nevi and a yearlong history of enlarging right preauricular mass. Examination revealed 2 congenital melanocytic nevi overlying a large, firm, mobile 2.7 × 2.5-cm subcutaneous mass with irregular borders. Pathology confirmed intradermal melanocyt...

Giant congenital melanocytic nevi (GCMN) are a rare occurrence. Gain-of-function mutation in the NRAS gene is found to be associated with GCMN, causing abnormal proliferation of embryonic melanoblasts. The two major complications associated with GCMN are malignant melanoma and neurocutaneous melanosis. Treatment of GCMN has conventionally been surgical. However, the role of NRAS inhibitors and ...

Sturge-Weber syndrome is a rare condition first described by Sturge in 1879 in a case report of an epileptic patient [1] . The association of intracranial calcifications was subsequently described by Weber in 1922, giving this condition its familiar eponym [2] . The classical findings include gyriform intracranial calcifications, congenital and usually unilateral capillary facial nevus, convuls...

Tissue expansion is an emerging trend in the reconstruction of various defects of the human body when there is insufficient adjacent tissue for direct closure of the defect or repair with a local tissue transfer. It is the most important armamentarium for aesthetic hair-bearing scalp reconstruction in cases of congenital or acquired defects. In this case, a large linear verrucous epidermal nevu...

A 13-year-old boy presented congenital, raised, yellowish colored plaques with fi broelastic consistency, which were velvety in appearance, alopecic, with clearly defi ned limits and sulci or well-marked meandering invaginations, a cerebriform appearance on the upper part of the right ear, accompanied by alopecia in the temporomandibular region-parietal. The lesion was asymptomatic. Histopathol...

Congenital hemidysplasia with ichthyosiform nevus and limb defects (CHILD) syndrome is a rare X-linked hereditary disorder. Presentation varies from ichthyosiform nevus to complete limb amelia. We present a 17-year-old adolescent girl who presented with a 16-cm exophytic mass of the right foot that had been growing for 7 years as well as knee contracture. Deformed nails with onychorrhexis were ...

Nevus lipomatosus cutaneous superficialis is a rare idiopathic hamartomatous anomaly of the skin characterized by the presence of clusters of mature fat cells among the collagen bundles of the dermis. The classic, or solitary type, presents with asymptomatic soft, skin-colored to yellow papules or nodules. We report the case of a 12-year-old boy with congenital, classical nevus lipomatosus cuta...