BACKGROUND Mucopolysaccharidosis type I (MPS-I) is a lysosomal storage disorder characterized by progressive multi-organ disease. The standard of care for patients with the severe phenotype (Hurler syndrome, MPS I-H) is early hematopoietic stem cell transplantation (HSCT). However, skeletal disease, including hip dysplasia, is almost invariably present in MPS I-H, and appears to be particularly...

BACKGROUND AND PURPOSE Earlier studies have suggested that the hip extension angle and the hip flexor moment in walking are affected by hip dysplasia, but to our knowledge there have been no reports on running or evaluations of self-reported health. We evaluated differences in walking, running, and self-reported health between young adults with symptomatic hip dysplasia and healthy controls. ...

Bernese periacetabular osteotomy (PAO) has several advantages dealing with adolescents and adults acetabular dysplasia. The authors introduced the details and steps performing PAO, with attached video and schematic diagram which demonstrates a perfect PAO in efficiency and accuracy. The patient is an 18-year-old girl, complaining hip pain on the left side for 6 months. Physical examination show...

Objectives: The overall aim of this study is to evaluate the incidence acetabular dysplasia in asymptomatic Sudanese adults. Methods: This a cross-sectional population-based study, which includes radiographic examination Hip. A total 240 hips are studied scout view routinely done patients undergoing CT KUB. morphology acetabulum assessed by measuring center edge angle (CEA), angle, depth width ...

Trevor disease or dysplasia epiphysealis hemimelica (DEH) is an extremely rare condition with incidence of about 1:1,000,000. Male to female ratio of reporting case is 3:1, and usually diagnosed between two and eight years old. It usually affects the medial portion of the joint, but lateral involvement is not uncommon. Hip-joint was affected in less than 4% of existing cases in the literature. ...

Residual hip dysplasia is one of the most common causes of secondary osteoarthritis of the hip joint. It is suggested that excessive hip joint contact stress due to small weight-bearing area is an important precipitating factor for the development of hip arthrosis (Hadley et al., 1990; Hipp et al., 1999; Maxian et al., 1995). Dysplasia of the hip refers to mechanical deformations and deviations...

Developmental dysplasia of the hip is a common musculoskeletal condition in newborns. Infants with developmental dysplasia of the hip, whether treated or untreated, have a higher incidence of early-onset hip osteoarthritis in adulthood. Evidence to support universal screening by physical examination or ultrasonography is limited and often conflicting. The U.S. Preventive Services Task Force fou...

This study explored the surgical method and short-term clinical effect of a greater trochanter osteotomy along with cementless artificial total hip arthroplasty in the treatment of Crowe type IV developmental dysplasia of the hip. The authors conducted a retrospective analysis of 18 patients (22 hips) with Crowe type IV dysplasia who were seen between June 2008 and August 2010. After undergoing...

Angel-shaped phalango-epiphyseal dysplasia is characterized by the angel shape of the middle phalanx and severe coxarthrosis in adult life. This osteochondrodysplasia shows a further variety of heterogeneous multiple epiphyseal dysplasias. It also shows a late and dysplastic development of the femoral head that leads to osteoarthrotic changes with severe hip pain and gait disturbance. In this r...

1. Hip dysplasia in German Shepherd Dogs, half of which could be expected to develop detectable hip dysplasia by 1 yr of age, was not observed at birth. This was based on the disection and gross examination of the pelves of eighty-seven neonatal pups. Minor ligamentous changes which may suggest beginning hip dysplasia were seen in three pelves from pups 30 days old. The round ligament seems to ...