Pseudocoarctaion is a rare congenital anomaly due to elongation of aortic arch. The exact etiology is still uncertain. It may be associated with other congenital cardiac and vascular anomalies. We report an unusual case of pseudocarctation associated with aberrant right subclavian artery, left SVC and multiple saccular aneurysms in the kinked arch and we feel that this is the first documented c...

The case of a 7-year-old female with a congenital left main coronary arteriovenous fistula to the right superior cavo-atrial junction, presenting with congestive cardiac failure, is reported for its rarity. The surgical importance of this anomaly is highlighted.

Unilateral pulmonary artery agenesis (UPAA) is an uncommon congenital anomaly and most patients present in neonatal period with respiratory symptoms. Left-sided pulmonary artery agenesis is less frequent than right-sided and is sometimes associated with cardiac anomalies. We report a patient with a history of repaired ventricular septal defect, who presented with cough and hemoptysis and the di...

We describe a case report of a patient with cardiac arrest and Ebstein's anomaly. This case report shows us necessity for arrhythmia evaluation and sudden death risk stratification even in asymptomatic patients. Prophylactic ICD implantation in this patient population is limited to observational studies and the selection of patients is impeded by the absence of randomized trials and weak predic...

Anomalous right coronary artery from left coronary sinus can have dynamic narrowing and kinking causing symptoms of myocardial ischemia and sudden cardiac death. Surgical repair of the anomaly is required in the symptomatic patient because of risk of ischemia or ventricular arrhythmia. Asymptomatic incidentally diagnosed low-risk patients can be closely followed up with exercise restriction as ...

Unruptured aneurysm of sinus of Valsalva (ASV) is a rare congenital anomaly. We describe a case of multiple unruptured ASV involving right and left aortic sinuses causing congestive cardiac failure in a 16-year-old boy who underwent successful surgical repair.

We present herein a case of cough-induced nonsustained ventricular tachycardia for which we found no definitive explanation. It could be an anomaly, but this so far unreported clinical fact is worth noting. Notwithstanding this interesting case, we believe that cough can be recommended as a safe and efficacious technique for overcoming hypotensive cardiac arrhythmias.

Double aortic arch is a congenital anomaly that is rarely found in adults. Typically, this is treated in infancy secondary to symptoms. We describe the treatment of an asymptomatic adult male that was diagnosed with double aortic arch during cardiac catheterization.

Truncus arteriosus (TA) is a rare cardiac anomaly constituting less than 1% of all congenital heart defects. Its association with complete atrioventricular septal defect (AVSD) is extremely unusual and only 12 cases diagnosed postnatally or postmortem have been reported so far. We describe the first case of truncus arteriosus with AVSD to be diagnosed prenatally by fetal echocardiography.

A 10-year-old girl presented with sudden onset recurrent ventricular tachycardia and symmetrical distal peripheral gangrene. She also had pulmonary thromboembolism and cerebral sinus venous thrombosis. Investigations revealed anemia, hemolysis, hypocomplementemia, and elevated IgM anti-beta2 glycoprotein antibody levels. Electrocardiogram and echocardiogram suggested features of a rare cardiac ...