The case reported herein consists of nodular pulmonary amyloidosis presenting with unusual cystic radiological features which reveal a pulmonary localisation of an extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue (MALT lymphoma). The present case is the first to report a radiological presentation of nodular pulmonary amyloidosis in the absence of Sjögren's syndrome....

Chronic subdural hematoma (CSDH) is a condition frequently seen in neurosurgical practice, especially among the elderly. It is often preceded by head injury, even a trivial trauma. Light chain (AL) amyloidosis is a disorder involving extracellular tissue deposition of misfolded native proteins called amyloids. The several types of amyloidosis differ by source of proteins, organ involvement, tre...

Secondary amyloidosis associated with systemic lupus erythematosus has rarely been reported. A 57-year-old female had been diagnosed as having possible systemic lupus erythematosus, although her clinical course was not typical. About one year after the diagnosis, treatment was begun with prednisolone because of progressive renal dysfunction, thrombocytopenia and low serum levels of complements....

Crescentic glomerulonephritis is a rare complication of AA amyloidosis. There are no clinical case reports of this complicating AL amyloidosis. A 67-year-old man developed rapidly progressive glomerulonephritis (RPGN) on a background of primary AL amyloidosis and IgGkappa multiple myeloma. Investigations for causes of glomerulonephritis were negative, and a renal biopsy confirmed crescentic glo...

AMYLOIDOSIS is a disease characterized by deposition of amyloid proteins in various body tissues. The natural history of primary amyloidosis is poorly understood, and the clinical diagnosis is often not made until the disease is far advanced. There is a high prevalence of conduction disturbances associated with this disease, and heart-related problems are a frequent cause of death for patients ...

Although systemic amyloidosis of amyloid-associated protein (AA) type (secondary or reactive amyloidosis) frequently involves the liver, it rarely causes clinically apparent liver disease. Mild elevation of alkaline phosphatase and hepatomegaly are the most common biochemical and clinical findings, respectively. We report a case of systemic amyloidosis of AA type, which clinically presented as ...

Introduction In major reviews of amyloidosis (Glenner, Terry and Isersky, 1973; Stirling, 1975) psoriasis is not listed as one of the predisposing causes nor is it mentioned as an aetiological factor in renal amyloidosis (Heptinstall, 1974). Case reports have drawn attention to amyloidosis in patients with pustular psoriasis (Berger, 1969; Mackie and Burton, 1974) and psoriatic arthritis (Reed ...

Objective: We aimed to improve the understanding and analysis of primary urinary bladder amyloidosis by discuss its clinical presentation, diagnosis and treatment. Method: We described one case of primary bladder amyloidosis and briefly discuss the management. We also conducted a systematic review of primary urinary bladder amyloidosis. Results: Transurethral resection was performed and follow-...

Amyloidosis is an uncommon disease that is characterized by abnormal extracellular deposition of misfolded protein fibrils leading to organ dysfunction. The deposited proteins display common chemical and histologic properties but can vary dramatically in their origin. Kidney disease is a common manifestation in patients with systemic amyloidosis with a number of amyloidogenic proteins discovere...

AL amyloidosis is a disease in which immunoglobulin L chain is deposited in multiple organs, and the prognosis of cardiac amyloidosis is extremely poor. Although several treatments based on that for multiple myeloma, have been performed, there is no clear evidence that cardiac function is improved. We report a case of AL cardiac amyloidosis with moderate cardiac dysfunction for which we perform...