Glycogen storage disease type III (GSD-III), an autosomal recessive disease, is caused by deficient glycogen debranching enzyme (GDE) activity. We identified three polymorphic markers in the GDE gene using single strand conformation polymorphism (SSCP) analysis and DNA sequencing. They were -10G/A in the 5' non-translated region of exon 3,2001 + 8C/T in intron 16, and 3199C/T (P1067S) in exon 2...

The dielectric permittivity, 3 0, and the loss factor, 3 00, of dry poly(2-hydroxyethyl methacrylate) were measured using a dielectric analyzer in the frequency range of 0.1 Hz to 100 kHz and between the temperature range of K150 to 275 8C. The dielectric response of the sub-Tg g transition of PHEMA has been widely studied before but little to no DEA data above 50 8C is present in the literatur...

Fine, monophasic silicon carbide powder has been synthesized by direct solid-state reaction of its constituents namely silicon and carbon in a 2.45 GHz microwave field. Optimum parameters for the silicon carbide phase formation have been determined by varying reaction time and reaction temperature. The powders have been characterized for their particle size, surface area, phase composition (X-r...

Background: Despite highly effective treatments to cure hepatitis C, almost 80% of chronically HCV-infected people are not treated, as they unaware their infection. Diagnostic rates and linkage care must be substantially improved reverse this situation. The HCV core antigen (HCVcAg) is a conserved protein that can detected in the blood patients indicates active Aim: To produce murine monoclonal...

Modern hydroponic substrates have contributed significantly to the popularity and progress of cultivations worldwide, nevertheless, their development, transportation, disposal often come at a significant environmental cost. Here we investigate feasibility partial total replacement conventional organic growing media constituents, such as cocodust (C), in 20% perlite (P) 80% substrate (hereafter ...

Bromomaleimides have recently been shown to act as small, versatile scaffolds for the controlled assembly of thiolated biomolecules. They present three points of chemical attachment, thereby allowing the modular construction of multifunctional bioconjugates. The bromomaleimide scaffold introduces no new chiral centres to the final construct and, in contrast to disulfide linkages, bromomaleimide...

Water wetting on a hydrophobic surface at ambient conditions is disallowed by the non-polar nature of the surface and high vapor pressure of water. However, the presence of sub-millimeter sized hydrophilic patches allows the waxy wings of desert beetles to become wettable by morning mist. Herein, we show that a sprinkle of graphene oxide nanoflakes (nanoGOs) is effective in condensing water nan...

This article discusses the performance of ZrO2-supported size-selected Pt nanoparticles for the decomposition of methanol, ethanol, 2-propanol, and 2-butanol. The potential of each alcohol for the production of H2 and other relevant products in the presence of a catalyst is studied in a packed-bedmass flow reactor operating at atmospheric pressure. All the alcohols studied show some decompositi...