نتایج جستجو برای: y microdeletion

تعداد نتایج: 495553  

Journal: :The journal of histochemistry and cytochemistry : official journal of the Histochemistry Society 2012
Anja Weise Kristin Mrasek Elisabeth Klein Milene Mulatinho Juan C Llerena David Hardekopf Sona Pekova Samarth Bhatt Nadezda Kosyakova Thomas Liehr

The widespread use of whole genome analysis based on array comparative genomic hybridization in diagnostics and research has led to a continuously growing number of microdeletion and microduplication syndromes (MMSs) connected to certain phenotypes. These MMSs also include increasing instances in which the critical region can be reciprocally deleted or duplicated. This review catalogues the cur...

2017
Prafulla S. Ambulkar Sunil S. Pande

Genetic factors cause about 15% of male infertility and microdeletions of Y chromosome is one of the genetic causes in idiopathic infertile men. Azoospermia factors (AZFa, AZFb, and AZFc) on Yq long arm are most important for spermatogenesis. For analysis of microdeletions in the AZF regions by sequence-tagged-site (STS) PCR is important screening method for infertility. An attempt has been mad...

Journal: :Molecular syndromology 2010
L A Praxedes F M Pereira J F Mazzeu S S Costa D R Bertola C A Kim A M Vianna-Morgante P A Otto

We report on a patient with NF1 microdeletion and clinical manifestations that fulfill the diagnostic criteria for neurofibromatosis type 1 but also presenting features reminiscent of Proteus syndrome.

Journal: :Developmental medicine and child neurology 2012
Russell C Dale Padraic Grattan-Smith Michelle Nicholson Greg B Peters

AIM Chromosome microarray (CMA) can determine copy number variants such as microdeletions or microduplications. Microdeletions of movement disorder genes including epsilon-sarcoglycan (SGCE) and thyroid transcription factor-1 (TITF1) have been described in patients with myoclonus dystonia and benign hereditary chorea respectively. We examined whether CMA is a valuable tool in the investigation ...

2017
Hong‐Dan Wang Lin Liu Dong Wu Tao Li Cun‐Ying Cui Lian‐Zhong Zhang Cheng‐Zeng Wang

BACKGROUND Little information is available regarding the penetrance of 1q21.1 copy number variants (CNVs). In the present study, we explored the clinical significance of 1q21.1 microdeletion or microduplication. METHODS In four families, chromosome karyotype was analyzed using G-banding karyotype analysis technology. CNVs were detected using array-comparative genomic hybridization (aCGH) and ...

2010
Krzysztof Flisikowski Heli Venhoranta Joanna Nowacka-Woszuk Stephanie D. McKay Antti Flyckt Juhani Taponen Robert Schnabel Hermann Schwarzenbacher Izabela Szczerbal Hannes Lohi Ruedi Fries Jeremy F. Taylor Marek Switonski Magnus Andersson

Congenital malformations resulting in late abortions and stillbirths affect the economic wellbeing of producers and the welfare of cattle in breeding programs. An extremely high incidence of stillbirths of "half-sized" calves of normal karyotype and uninflated lungs was diagnosed in the progeny of the Finnish Ayrshire (Bos taurus) bull--YN51. No other visible anatomical abnormalities were appar...

Journal: :Journal of medical genetics 2010
S Spengler N Schönherr G Binder H A Wollmann S Fricke-Otto R Mühlenberg B Denecke M Baudis T Eggermann

Silver-Russell syndrome (SRS) is a heterogeneous disorder associated with intrauterine and postnatal growth restriction, body asymmetry, a relative macrocephaly, a characteristic triangular face and further dysmorphisms. In about 50% of patients, genetic/epigenetic alterations can be detected: >38% of patients show a hypomethylation of the IGF2/H19 imprinting region in 11p15, whereas the additi...

2012
Heather C Mefford Jill A Rosenfeld Natasha Shur Anne M Slavotinek Victoria A Cox Raoul C Hennekam Helen V Firth Lionel Willatt Patricia Wheeler Eric M Morrow Joseph Cook Rachel Sullivan Albert Oh Marie T McDonald Jonathan Zonana Kory Keller Mark C Hannibal Susie Ball Jennifer Kussmann Jerome Gorski Susan Zelewski Valerie Banks Wendy Smith Rosemarie Smith Lindsay Paull Kenneth N Rosenbaum David J Amor Joao Silva Allen Lamb Evan E Eichler

BACKGROUND Chromosome 15q24 microdeletion syndrome is a rare genomic disorder characterised by intellectual disability, growth retardation, unusual facial morphology and other anomalies. To date, 20 patients have been reported; 18 have had detailed breakpoint analysis. AIM To further delineate the features of the 15q24 microdeletion syndrome, the clinical and molecular characterisation of fif...

Journal: :Archives of otolaryngology--head & neck surgery 2009
Isabelle Rouillon Nicolas Leboulanger Gilles Roger Michel Maulet Sandrine Marlin Natalie Loundon Marie France Portnoï Francoise Denoyelle Erea Noel Garabédian

OBJECTIVE To evaluate the results of velopharyngoplasty for velopharyngeal insufficiency (VPI) in relation to 22q11 deletion or nonsyndromic VPI. DESIGN Retrospective study. SETTING Academic medical center. PATIENTS Eleven of 45 patients with 22q11 microdeletion (group 1) and 9 patients without 22q11 microdeletion (group 2) with noncleft VPI (hypoplastic velum or hypodynamic velopharynx a...

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