we report the case of a three-year-old girl who complained from dysphagia and post-prandial vomiting since she was 6months old. several diagnostic work-ups were performed for her problem. upper gi endoscopy was normal but barium swallow revealed an external pressure effect over upper part of the esophagus (figure 1) and the ct angiography of thoracic aorta showed that this external pressure eff...

Pseudocoarctaion is a rare congenital anomaly due to elongation of aortic arch. The exact etiology is still uncertain. It may be associated with other congenital cardiac and vascular anomalies. We report an unusual case of pseudocarctation associated with aberrant right subclavian artery, left SVC and multiple saccular aneurysms in the kinked arch and we feel that this is the first documented c...

Persistent primitive hypoglossal artery (PPHA) is a recognised, albeit infrequent, intracranial vascular anomaly usually detected during angiography. Its presence is associated with an increased incidence of aneurysm, arteriovenous malformation and ischaemic stroke. A unique case of PHHA discovered during autopsy is described. Additionally, the significance of PPHA in neuroscience is discussed ...

Arteriovenous malformations (AVMs) are the most common spinal vascular anomaly. The majority are intradural and are supplied by the spinal arteries. This paper presents an unusual A VM that was fed by the lumbar arteries and was located totally in the extradural space; in fact, its drainage enlarged the internal vertebral venous plexus, resulting in its clinical presentation as a right lumbar r...

A case of Wolff-Parkinson-White syndrome type A with coexisting ipsilateral bundle branch block is presented. The diagnosis was suspected because of subtle electrocardiographic changes and was confirmed at electrophysiological study. Necropsy showed a vascular anomaly of the coronary sinus that contained bundles of myocardial muscle which crossed the atrioventricular ring at a site that was con...

Double aortic arch (DAA) is a congenital vascular anomaly. The diagnosis was difficult till the child was symptomatic, and other causes were ruled out. We present the interesting images of a child of respiratory distress because of tracheal compression from DAA.

A case of the scimitar sign due to an anomaly of the right sided pulmonary vein with normal drainage into the left atrium was associated with an azygos continuation of the inferior vena cava. Digital subtraction angiography allows the identification of these rare congenital vascular malformations.

Heterotopic pancreas is normal pancreatic tissue that lacks anatomic and vascular continuity with the main body of the pancreas. Heterotopic pancreatic tissue is a rare congenital anomaly found usually in the stomach, duodenum, or jejunum and is rarely seen in the esophagus. This is a case of heterotopic pancreas found in the esophagus that was removed thorascopically.

A 13-year-old girl with Turner's syndrome and bleeding from intestinal venous ectasia is reported. The various types of vascular anomaly of the bowel associated with Turner's syndrome are discussed. Awareness of these anomalies may help prevent unnecessary laparotomy in children with this syndrome.

Horseshoe kidney (HSK) is the most common renal anomaly. Reports of the incidence of renal cell carcinoma (RCC) in HSK are conflicting. Very few cases of isthmus-located RCC have been reported in the literature. We report a unique case of an isthmus-located RCC. Proper vascular and tumor imaging prior to surgery is key to successful tumor removal.