Journal:
:iranian journal of allergy, asthma and immunology
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zahra alizadeh immunology, asthma & allergy research institute, tehran university of medical sciences, tehran, iran
mohammad reza fazlollahi immunology, asthma & allergy research institute, tehran university of medical sciences, tehran, iran
payman eshghi department of pediatrics department, mofid children hospital, shaheed beheshti medical university, tehran, iran
amir ali hamidieh hematology-oncology & sct research centre, shariati hospital, tehran university of medical sciences, tehran, iran
zahra pourpak immunology, asthma & allergy research institute, tehran university of medical sciences, tehran, iran
mohsen ghadami immunology, asthma & allergy research institute, tehran university of medical sciences, tehran, iran
severe congenital neutropenia (scn) is a rare primary immunodeficiency. different genes are found to be associated with scn, including ela2, hax1, was, gfi1, g-csfr. also, recently g6pc3 as a rare gene in scn has been reported. patients with g6pc3 often have cardiac and/or urogenital malformations. two patients with persistent severe neutropenia, recurrent infections and maturatio...
