نتایج جستجو برای: primary immunodeficiency disorders

تعداد نتایج: 1346891  

Journal: :Current Opinion in Hematology 2013

Journal: :Proceedings of the Royal Society of Medicine 1975

Journal: :Asian Pacific journal of allergy and immunology 2013
Pamela Pui-Wah Lee Yu-Lung Lau

Primary immunodeficiency disorders (PIDs) are rare genetic diseases of the immune system. With improving awareness of PIDs among clinicians, the number of patients diagnosed with PIDs is rising rapidly in Southeast Asia. However, delayed diagnosis remains common and adversely affects the prognosis of these patients. In this review, we provide simple phenotypic approach to the diagnosis of PIDs ...

Journal: :The Turkish journal of pediatrics 2011
Sayna Norouzi Zahra Movahedi Setareh Mamishi Maryam Monajemzadeh Nima Rezaei

Severe combined immunodeficiency (SCID) is a rare primary immunodeficiency disease, which renders patients prone to recurrent severe infections in early childhood. Herein, we present a five-month-old boy with SCID who was referred to our center with recurrent diarrhea, respiratory infection and lymphadenopathy. Immunological studies showed hypogammaglobulinemia and low number of T-cells, which ...

2015
Jin Li Silje F Jørgensen S Melkorka Maggadottir Marina Bakay Klaus Warnatz Joseph Glessner Rahul Pandey Ulrich Salzer Reinhold E Schmidt Elena Perez Elena Resnick Sigune Goldacker Mary Buchta Torsten Witte Leonid Padyukov Vibeke Videm Trine Folseraas Faranaz Atschekzei James T Elder Rajan P Nair Juliane Winkelmann Christian Gieger Markus M Nöthen Carsten Büning Stephan Brand Kathleen E Sullivan Jordan S Orange Børre Fevang Stefan Schreiber Wolfgang Lieb Pål Aukrust Helen Chapel Charlotte Cunningham-Rundles Andre Franke Tom H Karlsen Bodo Grimbacher Hakon Hakonarson Lennart Hammarström Eva Ellinghaus

Common variable immunodeficiency disorder (CVID) is the most common symptomatic primary immunodeficiency in adults, characterized by B-cell abnormalities and inadequate antibody response. CVID patients have considerable autoimmune comorbidity and we therefore hypothesized that genetic susceptibility to CVID may overlap with autoimmune disorders. Here, in the largest genetic study performed in C...

Journal: :Iranian journal of allergy, asthma, and immunology 2012
Asghar Aghamohammadi Hassan Abolhassani Payam Mohammadinejad Nima Rezaei

Recurrent and chronic infections in children are one of the most common reasons for physicians' visits that make a diagnostic challenge to pediatricians. Although the majority of referred children with recurrent infections are normal, underlying causes of recurrent infection such as atopy, anatomical and functional defects, and primary or secondary immunodeficiency must be considered in evaluat...

2013
Julian C. Knight

Our understanding of immunity has historically been informed by studying heritable mutations in both the adaptive and innate immune responses, including primary immunodeficiency and autoimmune diseases. Recent advances achieved through the application of genomic and epigenomic approaches are reshaping the study of immune dysfunction and opening up new avenues for therapeutic interventions. More...

Journal: :iranian journal of allergy, asthma and immunology 0
maryam nourizadeh asghar aghamohammadi seyed mohammad moazzeni mahdi mahdavi nima rezaei jamshid hadjati

predominantly antibody deficiencies are a category of primary immunodeficiency diseases, which consist of several rare disorders such as common variable immunodeficiency (cvid) and x-linked agammaglobulinemia (xla). we evaluated the effects of cvid and xla patients’ sera as a source of microenviromental factors on maturation and function of monocyte-derived dcs. blood was collected from 10 cvid...

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