Distal myopathy with rimmed vacuoles (DMRV) is an autosomal recessive or sporadic early adult-onset myopathy caused by mutations in the UDP-N-acetylglucosamine 2-epimerase and N-acetylmannosamine kinase (GNE) gene. Characteristic pathologic features of DMRV are rimmed vacuoles on muscle biopsy and tubulofilamentous inclusion in ultrastructural study. Presence of inflammation in DMRV is unusual....

This work describes a new procedure to obtain optimal molecular superposition based on quantum similarity (QS): the geometric-quantum similarity molecular superposition (GQSMS) algorithm. It has been inspired by the QS Aufbau principle, already described in a previous work, to build up coherently quantum similarity matrices (QSMs). The cornerstone of the present superposition technique relies u...

Context. Bright-rimmed clouds (BRCs) are isolated molecular clouds located on the edges of evolved HII regions. Star formation within these clouds may have been triggered through the propagation of photoionisation-induced shocks driven by the expansion of the HII region. Aims. The main focus of this paper is to investigate the current level of star formation within a sample of southern hemisphe...

As Prof. Wierzbicki said in his speech at JAIST Forum 2006, “we are living in times of an informational revolution and this revolution leads to a new civilization era, in which knowledge plays a more and more important role than just information. We might say a new knowledge civilization era is starting”. It is clear that, in order to keep sustaining competitive competencies, new knowledge and ...

Organizational culture has a considerable impact on investment and acceptance of a new technology system such as knowledge management and especially it can be led to success or failure of knowledge management programs in organization. According to scientific evidences, human characteristics are effective on knowledge management and the process of knowledge management by people contains their pe...

This study aims to understand the antecedents of knowledge sharing behavior amongst tenant firms in Science and Technology Parks (STPs) which has been highlighted as a key factor for the development of an epistemic culture of innovation in STPs. Components of a model of knowledge management leadership with a focus on knowledge sharing and innovative value creation in STPs are developed inspired...

The article is devoted to the role of information culture in ensuring effectiveness knowledge management at university. Based on ideas P. Drucker and I. Nonaka need for continuous self-education individual using professional collective experience process practical training, means improving efficiency are considered, particular, introduction innovative leadership models, research activity expans...