نتایج جستجو برای: merzbacher

تعداد نتایج: 317  

2008
J. J. Laukka M. I. Makki J. Y. Garbern

Introduction: Diffusion tensor imaging (DTI) is a non-invasive exam that can characterize the microstructural properties of the brain white matter through the molecular diffusion processes. The application of DTI to the central nervous system (CNS) can accurately discriminates among different CNS disease pathologies by evaluating the microstructural architecture of the axonal fibers and myelin ...

Journal: :Pediatrics 2014
Jessica Wishnew Kristin Page Susan Wood Leo Galvin James Provenzale Maria Escolar Kathryn Gustafson Joanne Kurtzberg

Pelizaeus-Merzbacher Disease (PMD) is a rare X-linked recessive leukodystrophy caused by mutations in the proteolipid protein 1 gene on the Xq22 chromosome. PMD is a dysmyelinating disorder characterized by variable clinical presentation and course. Symptoms range from mild motor deficits to progressive spasticity and neurologic decline resulting in death at an early age. There is no definitive...

2013
Cherie M Southwood Bozena Fykkolodziej Fabien Dachet Alexander Gow

Although activation of the innate and adaptive arms of the immune system are undoubtedly involved in the pathophysiology of neurodegenerative diseases, it is unclear whether immune system activation is a primary or secondary event. Increasingly, published studies link primary metabolic stress to secondary inflammatory responses inside and outside of the nervous system. In this study, we show th...

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