Anorectal malformation is a congenital anomaly and can be either isolated or associated. This often combined with other defects, in particular VACTERL-association (anomalies of the spine, anal region, heart, trachea, esophagus, kidneys extremities), which requires comprehensive diagnosis these patients. Congenital malformations gastrointestinal tract except for esophageal atresia are rare. The ...

Introduction: Congenital anomalies (CA’s) of most the gastrointestinal tract have been linked causally with prenatal or community cannabis exposure. Therefore, we studied this relationship in Europe. Methods: CA data were from Eurocat. Drug-use sourced European Monitoring Centre for Drugs and Drug Addiction. Income taken World Bank. Results: When countries increasing rates daily use compared th...

We analyzed the flow velocity pattern in the main pulmonary artery after Fontan operation in patients with tricuspid atresia (n = 10) or with single ventricle (n = 10) by means of a catheter-mounted velocity probe. The area underneath the velocity signal of the forward flow was integrated, and ratios of the portions during atrial systole and during the diastolic phase to the total area (Fa and ...

UNLABELLED Early differentiation of extrahepatic biliary atresia from intrahepatic cholestasis is important. Hepatobiliary scintigraphy is an excellent noninvasive investigation for ruling out extrahepatic biliary atresia. This study aimed at identifying the role of ursodeoxycholic acid (UDCA), a choleretic agent, in conjunction with hepatobiliary scintigraphy in differentiating extrahepatic bi...

To provide an objective rapid means of excluding extrahepatic biliary atresia (atresia), a hepatic index was devised from the ratio of the net hepatic to cardiac distribution of 99mTc diisopropyl iminodiacetic acid or methylbrom iminodiacetic acid between 2.5 and 10 minutes after injection. The hepatic index was compared with subjective assessment of abdominal scintigraphy performed repeatedly ...

Congenital left main coronary artery (LMCA) atresia is a rare anomaly and surgical revascularization is recommended once the diagnosis is confirmed. In some cases, LMCA atresia will coexist with other cardiac anomalies, mostly in pediatric patients. A 32-year-old woman had congenital LMCA atresia associated with patent ductus arteriosus (PDA), aortic regurgitation (AR), and moderate pulmonary h...

Nasal obstruction in neonates is a potentially fatal condition because neonates are obligatory nasal breathers. Bilateral choanal atresia is therefore a neonatal emergency. Several approaches for corrections of choanal atresia are available including the helium laser: YAG. A 5-year-old Chinese girl born with bilateral choanal atresia, had birth asphyxia that required intubation. She underwent m...

Uterine isthmus atresia is a rare Müllerian duct anomaly occasionally diagnosed in adolescents with primary amenorrhea and cyclic abdominal pain. A case presented of 14-year-old female monthly lower pain 2-year duration. Magnetic resonance imaging 3-dimensional ultrasound showed separation 10-mm fibrotic tissue between the cervical canal endometrial cavity. In an attempt to preserve reproductiv...

Reid, I. S. (1973). Archives of Disease in Childhood, 48, 952. Biliary tract abnormalities associated with duodenal atresia. The embryology of the duodenum and biliary tracts makes understandable those developmental abnormalities of the biliary tract that occur in association with duodenal atresia. In a series of 167 patients with intrinsic duodenal obstruction, a number also showed anomalies o...

OBJECTIVES The study goal was to evaluate the hearing follow up results in patients who underwent surgery for congenital aural atresia. We studied hearing results and correlated them with Jahrsdoerfer prognostic classification. Protocols management of unilateral and bilateral atresia auris are written considering to our results and other authors. METHODS We conducted a retrospective review of...