A polygamous Nigerian family with inherited skeletal cardiovascular anomalies (Holt-Oram syndrome) is described. Common to the affected individuals in this family were pectus excavatum and abnormalities of the thumbs. Atrial septal defect was proven by angiocardiography in one and clinically diagnosed in another member of the family. The mode of inheritance of the abnormalities in this family a...

Surgical repair of an anomalous right pulmonary artery arising from the ascending aorta is rare. Angiocardiography is the procedure of choice in establishing the diagnosis. Surgical correction of the defect is mandatory; otherwise most of these children die in refractory heart failure. The present paper reports the first successful anatomic repair without a graft in a 2-month-old baby. Five mon...

The 15-year experience of the cardiac clinic at this hospital from 1953 to 1967, with 429 children under 14 years of age with coarctation, was reviewed. The aortic valves of 119 available post-mortem specimens were re-examined, and the incidence of bicuspid valves and valvar stenosis determined. This necropsy incidence was then compared with the clinical incidence of aortic valvar disease in ch...

With the advent of modern cardiac surgery the clinical diagnosis of intramural thrombi, ball valve thrombi and myxomatous and other tumors in the left atrium has assumed great importance. It is shown here that a diagnosis of thrombosis within the left atrium is possible by angiocardiography. The angiocardiographic features of mural and ball valve thrombi of the left atrium and of left auricular...

Planar equilibrium radionuclide angiocardiography (ERNA) is used to determine global and regional measures of ventricular function (primarily left ventricular [LV] function) at rest and/or during exercise stress or pharmacologic intervention. These measures of ventricular function may include evaluations of ventricular wall motion, ejection fraction (EF), and other parameters of systolic and di...

Two cases of common pulmonary vein atresia (CPVA) are presented. In one, the diagnosis was suspected on clinical grounds, and in both it was c onfirmed by cardiac catheterization and angiocardiography. Surgical correction was attempted unsuccessfully in one. Prompt identification of the defect followed by immediate operation, using a technic of profound hypothermia and circulatory arrest, offer...

BACKGROUND To explore the role of contrast-enhanced magnetic resonance angiography (CE-MRA) in clinical routine for evaluating neonates with pulmonary atresia (PA) and to describe their pulmonary artery morphology and blood supply.CE-MRA studies of 15 neonates with PA (12 female; median weight: 2900 g) were retrospectively evaluated by two radiologists in consensus. Each study was judged to be ...