INTRODUCTION This study was conducted to address whether staged surgical intervention or primary repair would be preferred for treating patients with tetralogy of Fallot and small left ventricle. METHODS We retrospectively assessed 28 patients with tetralogy of Fallot and small left ventricle at the Chinese PLA 208th Hospital, Changchun, between January 2005 and December 2008. Of this cohort,...

OBJECTIVES To determine the effect and safeness of the right ventricle to pulmonary artery connection with occlusion of major aortopulmonary collaterals and pulmonary artery angioplasty to rehabilitate the hypoplastic pulmonary arteries in patients with pulmonary atresia and ventricular septal defect beyond the infant period. METHODS From December 2009 to August 2012, 37 consecutive patients ...

A rare case of neonatal Ebstein's anomaly with circular shunting was reported. A two-stage surgical procedure was performed, and the outcome was good. Razook JD. Repair of Ebstein's anomaly in the symptomatic neonate: an evolution of technique with 7-year follow-up. Rapid two-stage Starnes procedure for a symptomatic neonate with Ebstein anomaly. Ebstein's anomaly appearing in the neonate. A ne...

Glenoid hypoplasia is a relatively rare alteration that in most cases involves the pectoral girdle in a bilateral and symmetrical manner. In general, glenoid hypoplasia is associated with skeletal changes such as hypoplasia of the humeral head or changes in the morphology of the acromion and of the coracoid. We describe a rare case of unilateral glenoid hypoplasia without instability and not in...

Although it is well known that enamel hypoplasia commonly is observed in prematurely born, very low birthweight (VLBW) children, its pathogenesis is not understood clearly. One likely mechanism may be related to mineral deficiency, which may be diagnosed as radiological demineralization of the long bones. In this study, we compared the cortical area of the humerus as measured from neonatal radi...

Since its first description optic nerve hypoplasia has been identified with increasing frequency, and a range of associated problems have been described. The major neurological and endocrine associations are well established, but those factors that predispose to the development of optic nerve hypoplasia remain unclear. To understand the aetiology of these problems better, and to formulate a man...

Horseshoe lung (HL) is often associated with cardiovascular malformations such as scimitar syndrome and unilateral lung hypoplasia. In patients with HL, the hypoplastic lung is almost always located on the right side. Cases of HL with a hypoplastic left lung are extremely rare. In this paper, we describe a case of a one-day-old boy with HL involving left lung hypoplasia and perform a systematic...

SUMMARY Echocardiographic studies were performed on six patients with autopsy-proved aortic atresia and hypoplastic left ventricle and two patients with surgically proved tricuspid atresia and hypoplastic right ventricle. The findings were compared to those from the echograms of 50 normal newborns who served as a control group. The ultrasound measurements obtained in the normal newborns were as...

OBJECTIVE One and one half ventricle repair is a surgical option for congenital cardiac anomalies characterised by right ventricle (RV) hypoplasia and/or dysplasia. METHODS From March 1994 to March 2001, eight patients (mean age 9.1 years, range 7 months to 35 years) with hypoplastic and/or dysplastic RV underwent correction of their intracardiac anomaly in association with a BCPS (one and on...

PURPOSE In adults, sphenoid sinus agenesis is an extremely rare anomaly. The objective of this study was to investigate the prevalence of sphenoid sinus hypoplasia and agenesis using dental volumetric computed tomography (DVCT) in a population of Turkish individuals. MATERIALS AND METHODS DVCT scans in the axial, coronal and sagittal planes of the sphenoid sinus of 384 patients were examined ...