Cases of Henoch-Schönlein purpura and purpura nephritis accompanied by pulmonary hemorrhage are rare. Mild cases are easily ignored due to a lack of evident bleeding, and severe cases may be fatal. We have only treated one patient with Henoch-Schönlein nephritis (HSPN), a female child. The clinical manifestations were not evident, however, the imaging manifestations were clear. Finally, the pat...

Henoch-Schönlein purpura (HSP) was first described more than 200 years ago by Heberdon. It is the most common systemic vasculitis of childhood. Short and long term outcomes of HSP is generally favorable, with complete and spontaneous resolution of symptoms (1-3). Renal involvement occurs in 40%-60% of pediatric patients within 4 to 6 weeks of the initial presentation (1). It is the major cause ...

Henoch-Schönlein purpura (HSP) is the most common primary systemic vasculitis of childhood (1). It is generally considered a self-limited disease, and majority of patients improve completely (2,3). Shortand long-term outcomes of HSP are generally favorable, and predicted by the severity of initial manifestations and renal involvement (1,2). Henoch-Schönlein purpura nephritis (HSPN) is the major...

BACKGROUND AND PURPOSE Depending on the severity of the illness, thrombocytosis is found in about 60% to 70% of patients with Henoch-Schönlein purpura (HSP). Whether thrombocytosis is the result of an inflammatory reaction mediated by thrombopoietin (TPO) or other inflammatory cytokines such as interleukin (IL)-6 remains unknown. METHODS Thirty two patients who met the diagnostic criteria for...

how to cite this article: shiari r, tabatabaei nodushan smh, mohebbi mm, karimzadeh p, javadzadeh m. moyamoya syndrome associated with henoch-schönlein purpura. iran j child neurol. autumn 2016; 10(4):71-74. abstract some reports have shown the association between moyamoya syndrome and autoimmune diseases. herewith, we present a 3.5 yr old girl with henoch- schönleinpurpura (hsp) who was treate...

We herein describe the case of a 60-year-old man who presented clinical and histopathological evidence of Henoch-Schönlein purpura. Antineutrophil antibodies (ANCA) showed positive results on an enzyme-linked immunosorbent assay and immunofluorescence for anti-myeloperoxidase and anti-proteinase 3 antibodies. Dual positivity for both cytoplasmatic (C-ANCA) and perinuclear (P-ANCA) antineutrophi...

Primary vasculitides, where blood vessels are the primary site of inflammation, with the exception of Henoch Schönlein purpura (HSP) and Kawasaki’s disease (KD) are rare in childhood but when present, cause significant morbidity and mortality. This review provides an update on classification and presentation of rare vasculitides in children, through considering our experience in three cases in ...

Henoch-Schonlein Purpura (HSP) is systemic vasculitis in children, hallmark by inflammatory infiltration of polymonuclear leukocytes small blood vessels, followed IgA1 immune deposits. HSP prevalence approximately 3-27 cases per 100,000 children. The process causes an ischemia and hemorrhagic characterized non-thrombocytopenia purpura, arthralgia, gastrointestinal problems, kidney impairment. T...

Henoch-Schönlein purpura is a small vessel vasculitis which is uncommon in adults. The presentations of adult-onset disease are different from those seen in childhood. The commonly-recognised serious gastrointestinal complications of childhood are less well-documented in adults. We report three cases of adult-onset Henoch-Schönlein purpura with severe gastrointestinal involvement. All were men,...

Primary vasculitides, where blood vessels are the primary site of inflammation, with the exception of Henoch Schönlein purpura (HSP) and Kawasaki’s disease (KD) are rare in childhood but when present, cause significant morbidity and mortality. This review provides an update on classification and presentation of rare vasculitides in children, through considering our experience in three cases in ...