We present a case of an infant male born at 23 weeks' gestation with interrupted aortic arch (IAA) complex. treated the patient hypoxic gas ventilation to address developing systemic undercirculation in acute postnatal phase. As symptoms bronchopulmonary dysplasia evolved, was no longer required stabilize hemodynamics. The discharged home after undergoing palliative surgical procedure bilateral...

Objective: To determine the outcomes for a program that utilizes the double switch operation as the primary approach for congenitally corrected transposition. Methods: The records of 46 consecutive patients from a single institution who had undergone a double switch operation from October 1993 to March 2002 were reviewed. The records of 24 patients who were evaluated during the same period and ...

Primary LV dysfunction LV function with myocardial changes are invariably noted early in fetuses that develop HLHS. Possibly this is the initial disturbance (e.g fetal myocarditis) The abnormal aortic valve may be the result of inability of the LV to provide forward flow; the valve is closed by the pressure in the aorta provided from the pulmonary artery through the ductus arteriosus. Control A...

We present the first case of a successful Fontan completion in a patient with previous liver transplantation. An infant with polysplenia syndrome with a functional single ventricle and biliary atresia had been surgically managed by pulmonary artery banding, Kasai operation and living donor liver transplantation. Subsequently, the patient successfully underwent bidirectional cavopulmonary shunt ...

a spectrum of disease. In a small number of patients, the presence of pulmonic stenosis (congenital or acquired by pulmonary artery banding in infancy), a small ventricular septal defect, or a large atrial septal defect was not protective against the development of severe PVD. The findings of this study demonstrate the need for thorough hemodynamic evaluation of patients with complete transposi...