نتایج جستجو برای: progeroid syndrome

تعداد نتایج: 622026  

2017
Masaya Yamaga Minoru Takemoto Mayumi Shoji Kenichi Sakamoto Masashi Yamamoto Takahiro Ishikawa Masaya Koshizaka Yoshiro Maezawa Kazuki Kobayashi Koutaro Yokote

Werner syndrome (WS) is a rare inheritable progeroid syndrome caused by a mutation in the WRN gene. Although WS has been described as a characteristic appearance of very slender extremities with a stocky trunk, few studies have investigated the loss of muscle mass, fat mass distribution (body composition), and mobility according to age and sex. Therefore, the aim of this study was to precisely ...

Journal: :Trends in Glycoscience and Glycotechnology 1993

Journal: :PLoS Genetics 2006
Marieke van de Ven Jaan-Olle Andressoo Valerie B Holcomb Marieke von Lindern Willeke M. C Jong Chris I. De Zeeuw Yousin Suh Paul Hasty Jan H. J Hoeijmakers Gijsbertus T. J van der Horst James R Mitchell

How congenital defects causing genome instability can result in the pleiotropic symptoms reminiscent of aging but in a segmental and accelerated fashion remains largely unknown. Most segmental progerias are associated with accelerated fibroblast senescence, suggesting that cellular senescence is a likely contributing mechanism. Contrary to expectations, neither accelerated senescence nor acute ...

پایان نامه :دانشگاه آزاد اسلامی واحد علوم پزشکی تهران - دانشکده علوم پزشکی 1389

هدف: در این مطالعه به بررسی اثر تزریق کورتیکواسترویید در درمان infrapatellar fat pad syndrome در بیماران مراجعه کننده به درمانگاه ارتوپدی بیمارستان امیرالمومنین (ع) تهران در سال 1388 پرداختیم.روش مطالعه: این مطالعه به صورت یک بررسی مداخله ای (interventional) از نوع نیمه تجربی (quasi-experimental) انجام گردیده است. جامعه مورد بررسی شامل 60 نفر از افراد مبتلا به infrapatellar fat pad syndrome بود...

2015
Jean-Ha Baek Eva Schmidt Nikenza Viceconte Charlotte Strandgren Karin Pernold Thibaud J. C. Richard Fred W. Van Leeuwen Nico P. Dantuma Peter Damberg Kjell Hultenby Brun Ulfhake Enrico Mugnaini Björn Rozell Maria Eriksson

Hutchinson-Gilford progeria syndrome (HGPS) is a segmental progeroid syndrome with multiple features suggestive of premature accelerated aging. Accumulation of progerin is thought to underlie the pathophysiology of HGPS. However, despite ubiquitous expression of lamin A in all differentiated cells, the HGPS mutation results in organ-specific defects. For example, bone and skin are strongly affe...

Journal: :Toxicological sciences : an official journal of the Society of Toxicology 2009
Xuefeng Ren Sophia Lim Martyn T Smith Luoping Zhang

Werner syndrome (WS) is a rare autosomal progeroid disorder caused by a mutation in the gene encoding the WRN (Werner syndrome protein), a member of the RecQ family of helicases with a role in maintaining genomic stability. Genetic association studies have previously suggested a link between WRN and susceptibility to benzene-induced hematotoxicity. To further explore the role of WRN in benzene-...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید