It is well known that neurofibromatosis is one apparent etiology for the type of intracranial arterial occlusive disease known as moyamoya disease [1-4]. All previously reported cases of neurofibromatosis with moyamoya disease have had involvement only of the intracranial carotid circulation (supraclinoid internal carotid artery, middle cerebral artery, anterior cerebral artery) [1 -4]. We repo...