نتایج جستجو برای: lebers congenital amaurosis

تعداد نتایج: 120868  

2010
Donna S. Mackay Robert H. Henderson Panagiotis I. Sergouniotis Zheng Li Phillip Moradi Graham E. Holder Naushin Waseem Shomi S. Bhattacharya Mohammed A. Aldahmesh Fowzan S. Alkuraya Brian Meyer Andrew R. Webster Anthony T. Moore

PURPOSE To report the clinical phenotype in patients with a retinal dystrophy associated with novel mutations in the MER tyrosine kinase (MERTK) gene. METHODS A consanguineous family of Middle Eastern origin was identified, and affected members underwent a full clinical evaluation. Linkage analysis was performed using the Affymetrix 50K chip. Regions of homozygosity were identified. The posit...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2010
James S Friedman Bo Chang Daniel S Krauth Irma Lopez Naushin H Waseem Ron E Hurd Kecia L Feathers Kari E Branham Manessa Shaw George E Thomas Matthew J Brooks Chunqiao Liu Hirva A Bakeri Maria M Campos Cecilia Maubaret Andrew R Webster Ignacio R Rodriguez Debra A Thompson Shomi S Bhattacharya Robert K Koenekoop John R Heckenlively Anand Swaroop

Retinal degenerative diseases, such as retinitis pigmentosa and Leber congenital amaurosis, are a leading cause of untreatable blindness with substantive impact on the quality of life of affected individuals and their families. Mouse mutants with retinal dystrophies have provided a valuable resource to discover human disease genes and helped uncover pathways critical for photoreceptor function....

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