conclusions alterations were present in both the aspect and spacing of collagen fibrils and in the shape of elastic fibers. the present familial combination of scad and edsh, with almost similar ultrastructural features suggests a possible connection between both conditions. case presentation we present a woman with scad and her five close relatives showing obvious or suggestive signs of edsh. ...

arrhythmogenic right ventricular dysplasia/cardiomyopathy (arvd/c) is a congenital cardiac disease with myocardial involvement, most probably right ventricular (rv) dysfunction, accounting for 20% of sudden cardiac deaths. characterized by the fibro-fatty infiltration of the rv free wall, arvd/c presents in adolescents with ventricular arrhythmias and heart failure symptoms and as biventricular...

purpose : to report a case of congenital macular macrovessels case report : an 8-year-old girl was referred for decreased vision in her right eye. her best corrected visual acuity (bcva) in the right eye was 20/200 and in the left eye 20/20. anterior segment examinations were normal in both eyes. posterior segment examination of the right eye showed abnormal macrovessels crossing the macula and...

The study of pulmonary vessels has assumed great importance in the last decade since the advent of corrective surgery for congenital cardiac defects. Several papers have been written on the structure and state of these vessels, in utero, in neonatal life and during later years (Edwards, 1957; Civin and Edwards, 1951; Dammann and Ferencz, 1956a). These papers stress the basic differences in the ...

Climate change is impacting sea ice extent and thickness in the Canadian Arctic, creating an increase maritime accessibility that may accentuate risks related to ship operations due a mobility. The overall risk ships operating regions with mobile will vary significantly depending on class (i.e., level of strengthening) vessel. Several studies have examined implications for operations, but date ...

background: differences in the quantity and distribution of coronary veins between patients with ischemic and non-ischemic cardiomyopathy might affect the potential for the left ventricular (lv) lead targeting in patients undergoing cardiac resynchronization therapy (crt). in the current study, we assessed and compared the suitability of the coronary venous system for the lv lead placement in i...