نتایج جستجو برای: kearns sayre

تعداد نتایج: 927  

2017
Dinushi Dilanka Dikowita Thirunavukarasu Kumanan Muthusamy Malaravan Mahesan Guruparan

Background: Kearns Sayre Syndrome (KSS) is a rare mitochondrial disorder with systemic involvement characterised by skeletal, smooth and cardiac muscle dysfunction; pigmentary retinal changes; neurological and endocrine dysfunction. KSS arise from a large-scale deletion of mitochondrial DNA which typically occurs as a sporadic event. Recurrent cardiac syncope is one way of the initial presentat...

2014
Sherezade Khambatta Douglas L Nguyen Thomas J Beckman Christopher M Wittich

BACKGROUND Kearns-Sayre syndrome (KSS) is a rare mitochondrial cytopathy, first described at Mayo Clinic in 1958. AIMS We aimed to define patient and disease characteristics in a large group of adult and pediatric patients with KSS. METHODS We retrospectively searched the Mayo Clinic medical index patient database for the records of patients with KSS between 1976 and 2009. The 35 patients i...

2014
Pilar Quijada-Fraile Mar O’Callaghan Elena Martín-Hernández Raquel Montero Àngels Garcia-Cazorla Ana Martínez de Aragón Jordi Muchart Ignacio Málaga Rafael Pardo Pedro García-Gonzalez Cristina Jou Julio Montoya Sonia Emperador Eduardo Ruiz-Pesini Joaquín Arenas Miguel Angel Martin Aida Ormazabal Mercè Pineda María T García-Silva Rafael Artuch

BACKGROUND Kearns-Sayre syndrome (KSS) is a mitochondrial DNA deletion syndrome that presents with profound cerebral folate deficiency and other features. Preliminary data support the notion that folinic acid therapy might be useful in the treatment of KSS patients. Our aim was to assess the clinical and neuroimaging outcomes of KSS patients receiving folinic acid therapy. METHODS PATIENTS...

2016
Meng Yu Lei Yu Zhao-Xia Wang

DNA studies in patients with Kearns‑Sayre syndrome and chronic progressive external ophthalmoplegia. We appreciate the readers' interest and their comprehensive comments and advice about the article, [1] which mainly concerned details of the patients' information. In this paper, we reported 19 Kearns‑Sayre syndrome (KSS) patients whose diagnoses were in accordance with the current clinical diag...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید