Ellis-van Creveld syndrome is transmitted as an autosomal recessive trait. This syndrome is accompanied in 60% of cases with congenital heart disease, mostly single atrium or large ASD. Patients are mostly symptomatic, but in this rare case despite 68 years of age, the patient was free of symptoms except for complete heart block for which pacemaker was inserted

THE PRESENCE of complete heart block offers a good opportunity to study cardiovascular functions, since one of the major variables of cardiac activity, i.e., heart rate, is maintained constant.113 In addition, if a cardiac pacemaker is implanted in a heart for treatment of complete heart block,14-20 total control of the cardiac rate is achieved, thereby providing an excellent opportunity for st...

The optimal anaesthetic management of neonates with complete congenital heart block (CCHB) is unknown, as there is a low incidence of such cases. Neonates with CCHB often require surgery for the initiation of electronic pacing. In addition to the challenges of anaesthetising a neonate, this procedure is risky due to the potential for hypotension, arrhythmias and cardiac arrest. We herein presen...

A case of a 71-year-old male with congenital complete heart block is discussed. Patient remained asymptomatic with stable electrocardiograms.

background : in medical studies, when the joint prediction about occurrence of two events should be anticipated, a statistical bivariate model is used. due to the limitations of usual statistical models, other methods such as artificial neural network (ann) and hybrid models could be used. in this paper, we propose a hybrid artificial neural network-genetic algorithm (ann-ga) model to predictio...

To our knowledge, isolated dextrocardia in association with congenital complete atrioventricular heart block has not been previously reported. We report such a case, elaborate on the possible pathogenesis, and present our experience with management.