La fibromatose colli est une tumeur bénigne, rare, du muscle sternocléidomastoïdien, causant des torticolis congénitaux chez les nouveau-nés ou nourrissons. A ce jour, le mécanisme étiopathogénique de son apparition reste mal connu. Son diagnostic combine l’examen clinique et l’échographie qui permettent mettre en évidence un épaississement caractéristique muscle. Nous rapportons cas, diagnosti...

introduction: desmoid tumors are very rare, benign fibrous neoplasms arise from the musculoaponeurotic structures throughout the body.   case report: the patient was a   seven-year old boy with a large mandibular mass growing over a period of six months. his ct-scan showed a large mass, 13 cm in diameter in the cheek area extending to the neck and trachea. biopsy was compatible with desmoid fib...

Two molecular recombinants (EU-8 and K-3) constructed from ring-necked pheasant virus and UR2AV, the helper virus associated with avian sarcoma virus UR2, caused a high incidence of a hitherto unreported pathological condition in chick skeletal muscle. A disease spectrum was observed in which muscle was infiltrated by proliferating fibroblasts and caused white streaks, white diffuse areas, or w...

pachydermodactyly is a rare and benign disease that may be idiopathic, genetic, acquired as a response to repetitive trauma, or associated with several other acquired conditions often pushing the health caregiver to do a bunch of costly lab tests and diagnostic workups to rule out other entities. all health care givers must be aware about this disease for reassure the patients and cut unnecessa...

Infantile myofibromatosis (IM) is a rare benign tumor in children. It was first described as congenital fibrosarcoma. Later, sporadic cases were discussed, and in 1981, 61 cases were examined and named as IM. Three different forms were described: solitary, multicentric and visceral IM.1 Three quarters of soft tissue tumours in children and adolescents are benign, 95 % of them are fibromatosis, ...

Spectrum of Fibroblastic and Myofibroblastic Tumors When one considers soft tissue tumors in pediatrics, tumors of vascular (29%), neurogenic (15%), and myogenic (striated muscle, 14%) origin occur more often than fibroblastic-myofibroblastic tumors (12%). The spectrum of fibroblastic/myofibroblastic tumors is quite divergent from both clinical and histopathologic viewpoints (Table 1). These tu...

The pathogenesis of generalized fibromatosis still remains unknown, despite reports on association with estrogen receptors. This disease is classified into three types as follows: solitary fibromatosis, congenital generalized fibromatosis without visceral involvement, and congenital generalized fibromatosis with both cutaneous and visceral involvement. In most cases, the disease is sporadic, bu...

Introduction: Aggressive fibromatosis (desmoid tumor) is a locally invasive soft tissue lesion, composed of a monoclonal proliferation of benignappearing spindle (fibroblast like) cells. A subset of lesions contain a somatic mutation in the adenomatous polyposis coli (APC) gene (1). Familial Adenomatosis Polyposis (FAP) is an inherited pre-neoplastic condition that predisposes to colonic neopla...