BACKGROUND The cardiovascular system is the part of the fetal anatomy that most frequently suffers from congenital pathology. This study shows our preliminary experience with fetal cardiovascular magnetic resonance (CMR) to evaluate congenital cardiovascular abnormalities. METHODS Between January 2006 and June 2011, Prenatal routine obstetric ultrasound (US), echocardiography and CMR data fro...

BRONCHOGENIC CYSTS ARE UNCOMMON congenital lesions located within the mediastinum. These lesions usually are asymptomatic and rarely require surgical intervention. The authors present a unique case demonstrating intraoperative transesophageal echocardiographic evidence of superior vena cava (SVC) compression by a bronchogenic cyst without any preoperative clinical or sonographic evidence of vas...

Complex cyanotic congenital heart diseases with left isomerism are sometimes associated with atrioventricular nodal conduction disturbances that may need permanent pacing. Surgical palliation in such anatomy connecting the superior vena cava to the pulmonary artery precludes a transvenous access for an endocardial pacing lead to the ventricles. Epicardial leads in these patients fail if the pac...

Aorta-right atrial tunnel is a rare and distinct congenital anomaly. It is a vascular channel that originates from one of the sinuses of Valsalva with a tortuous course anterior or posterior to the ascending aorta, and terminates either in the superior vena cava or in the right atrium (RA). We report a 42-year-old female briefly with aorta-right atrial tunnel in which the left coronary artery a...

A 6-year-old female child sought medical service due to a gastrointestinal malformation. During medical follow-up, partial absence of the inferior vena cava was diagnosed, a rare congenital alteration affecting the vascular drainage from the inferior segment of the body. Imaging exams were accomplished, contributing to evaluation and description of the case. Conservative treatment with oral ant...

progressive osseous heteroplasia is a rare inherited disease that begins with skin ossification and proceeds into the deeper connective tissues. the disease should be distinguished from other genetic disorders of heterotopic ossification including fibrodysplasia ossificans progressiva (fop) and albright hereditary osteodystrophy (aho). we report a case of progressive osseous heteroplasia in a t...

The Glenn operation involving anastomosis of the superior vena cava to the pulmonary artery has been performed for palliative operations of many cyanotic congenital heart diseases in addition to the single ventricle since the 1960s. The classic procedure is done via median sternotomy and cardiopulmonary bypass. The benefits of this procedure without the use of cardiopulmonary bypass remain mixe...

Scimitar syndrome is a rare congenital anomaly characterized by total or partial anomalous pulmonary venous drainage of the right lung to the inferior vena cava. We present a seven year old girl with a systolic murmur who was diagnosed as having a Scimitar syndrome with unusual drainage of the right pulmonary veins. The unique technique of surgery in this patient was appropriate to the unusual,...