Previously, complete absence of an interatrial septum (IAS) was thought to be a form of an atrioventricular septal defect involving the cleft mitral valve and interventricular communication. Ellis et al. (1) defined this condition as common atrium (CA). This congenital cardiac anomaly is especially observed in association with heterotaxy syndrome. Levy et al. (2) reported a case of complete abs...

Objectives . This study was conducted to investigate the presentation and outcome of patients with Ebstein's anomaly of the tricuspid valve . Background. Ebstein's anomaly may present at any age and has a highly variable clinical course . Previous natural history studies have been based on clinical and angiographic diagnosis and have included mainly older children and adults . Echocardiography,...

Situs ambiguous anomaly is a rarely encountered condition in clinical practice that is characterized by the presence of multiple congenital anomalies relevant to intraabdominal organs and the cardiovascular system. While this syndrome is mostly diagnosed as a serious cyanotic cardiac disease in the first year of life, only 5% may survive beyond five years of life, and it can be a diagnostic cha...

Critical congenital pulmonary stenosis with intact interventricular septum is a cyanotic and potentially lethal neonatal cardiac anomaly. Percutaneous transcatheter balloon valvuloplasty for critical often presents technical difficulties due to supra-systemic pressure in right ventricle. Using transjugular approach instead of the femoral vein helps dealing this issue. We describe successful use...

Left ventricular non-compaction (LVNC) is a rare congenital cardiomyopathy characterized by the presence of an extremely thickened endocardial layer with prominent trabeculations and deep recesses in communication with ventricular chamber and determining a typical spongeous aspect [1]. Noncompaction of the ventricular myocardium is thought to be a congenital arrest of endomyocardial embryogenes...

M-mode echocardiographic studies were performed in 11 patients, most of them adults, with Ebstein's anomaly of the tricuspid valve, proven by cardiac catheterisation. Simultaneous recordings of the tricuspid and mitral valves were obtained in all cases, the transducer position being outside the left midclavicular line in seven patients. Tricuspid valve closure followed mitral valve closure in a...

The VACTERL association, co-occurrence of vertebral, anorectal, cardiac, tracheoesophageal, genitourinary, and limb malformations, is a rare congenital anomaly. Several cardiac anomalies have been reported as a part of the VACTERL association, particularly ventricular and atrial septal defects. Pulmonary artery sling is a rare congenital abnormality in which the left pulmonary artery arises fro...

IN 1930, Wolff, Parkinson, and Vhite 1 described a syndrome characterized by an abnormal and distinctive type of electrocardiogram and an associated tendency for sudden attacks of supraventricular arrhythmias. There has been controversy regarding the priority of the description of the electrocardiographic pattern, and widely differing theories of the pathogenesis of the syndrome have been propo...

Persistent atrial standstill occurred in a father and his youngest son with familial Ebstein's anomaly. In both cases routine electrocardiograms showed no atrial electrical activity and cross sectional echocardiograms showed inferior displacement of the septal tricuspid leaflet and tethering of the tricuspid leaflets to the right ventricle. The father had a cerebral embolism and died of a myoca...