BACKGROUND Behcet's disease (BD) is a well-known cause of Budd-Chiari syndrome (BCS). Data are lacking on the presentation and outcome of BCS related to BD. METHODS We investigated the relationship between BD and BCS in 14 patients with both diseases and compared the results to 92 BCS patients without BD. RESULTS Male gender (p = 0.003), North African origin (P = 0.007) and inferior vena ca...