Patients with Urbach-Wiethe disease constitute a unique nature experiment as more than half have bilaterally symmetrical damage in the amygdaloid region. Ten such patients were studied neuropsychologically and, nine of them, neuroradiologically with static (CT) and functional imaging techniques [single-photon emission computed tomography (SPECT) and PET]. Their principal bilateral amygdala dama...

Abstract Sr 3− x Pb Fe 2 TeO 9 ( = 1.50, 1.88 and 2.17) were synthesized in polycrystalline form via the solid-state reaction route air, studied at room temperature using powder X-ray diffraction ultraviolet visible spectroscopy techniques. The crystal structures resolved by Rietveld refinement method; 1.50 adopt a tetragonal phase (space group I 4/ mmm ) while 2.17 adopts hexagonal R <m:math x...

Two patients with lipoid proteinosis are reported in whom paranoid symptoms were the presenting feature. Both had a long standing impairment of memory and bilateral medial temporal lobe calcification demonstrated by CT scan. Possible associations between the anatomical site of these lesions and the neuropsychiatric manifestations are discussed.

Lipoid proteinosis is a rare hereditary disease which often results in bilateral calcifications in the medial temporal region. Thirty-four adults living with lipoid proteinosis (>10% of the world population) were extensively assessed with standardized neuropsychiatric and neuropsychological measures. Of these, 27 patients representing a homogenous group living in the Northern Cape were matched ...

A case of lipoid proteinosis presented with multiple papular lesions on the face and hoarseness of voice from early infancy. Five sibs of the patient were affected and one had died early in infancy, probably because of laryngeal obstruction.

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The continued production of new dentate granule cells throughout life has led to the idea that neurogenesis critically modulates hippocampal memory function. Consistent with this view, many studies have shown that experimental reduction of adult neurogenesis impairs hippocampal memory formation. However, impairments are not universally observed following suppression of adult neurogenesis. A new...

Polycarbazole (PCz) has been synthesized by chemical oxidation method using APS as an oxidizing agent and PCz/CuO PCz/Fe2O3 nanocomposites in situ polymerization for different wt% of CuO Fe2O3 at room temperature. XRD patterns confirmed crystalline nature samples. FTIR indicated strong interaction between PCz nano fillers. The morphological optical absorption studies were carried out SEM UV–Vis...

We study the crystalline structure and absorption spectra for zinc oxide films with different levels of yttrium doping. The are deposited on glass substrates, using radio-frequency magnetron sputtering. estimate concentration free charge carriers show that 'blue' shift fundamental edge in ZnO:Y increasing doping level (up to 4.7 wt. %) is explained by Burstein-Moss effect. At higher concentrati...