Fifty-six patients with tricuspid atresia and decreased pulmonary blood flow received a systemic-to-pulmonary artery anastomosis as a preliminary operation. Thirty-five had a Waterston shunt, 12 a Blalock-Taussig anastomosis, and nine various other procedures. The age at operation ranged from 2 days to 10 years (median 4.5 months). Pulmonary atresia was present in eight newborn infants. Four pa...

Definition of “functionally single ventricle” includes a wide spectrum of anatomical variants such as double inlet left or right ventricle, mitral or tricuspid atresia, unbalanced atrioventricular canal, heterotaxy syndrome with one normally developed ventricle or other congenital heart defects with severe hypoplasia of one of the ventricles [2]. Anatomical and hemodynamic abnormalities in thes...

PURPOSE Outcomes in 6 neonates with pulmonary atresia and intact ventricular septum (PAIVS) undergoing radiofrequency pulmonary valvulotomy and valvuloplasty (RPVV) were reported to identify the factors favorable for RPVV as the treatment of choice. MATERIALS AND METHODS From May 2000 to January 2008, 6 patients with PAIVS were included in this retrospective study. They were aged 1 day to 90 ...

This is a report on the anatomical findings of 6 cases of typical Ebstein's anomaly found in a review of 1300 autopsy specimens. In addition 2 cases with pulmonary atresia and 1 with atresia of the malformed tricuspid valve showing morphologically similar anomalies were found, as well as 29 cases with tricuspid valvular dysplasia (21 of them coexisting with pulmonary atresia with intact ventric...

Seven cases of single ventricle, six cases of hypoplasia of the right heart (tricuspid atresia), and one case of hypoplasia of the left heart were investigated with reflected ultrasound. In hypoplasia of the right heart there was abnormal anterior movement of the mitral valve; in hypoplasia of the left heart, abnormal anterior movement of the tricuspid valve, and in single ventricle, similiar m...

Tricuspid atresia (TAt) is a complex congenital heart defect (CHD) characterized by the absence of the tricuspid valve and right ventricular hypoplasia requiring surgery in childhood, the Fontan procedure. We present a case of a 21-year-old male with TAt and cystic fibrosis (CF), who underwent a Fontan procedure in childhood, presenting to an adult CF clinic with severe deterioration in his res...

Wheadey, D. J., Prusty, S., and Ross, D. N. (1974). Thorax, 29, 617-623. Reconstruction of right ventricular outflow with a valved homograft conduit. Since 1966 a conduit of homograft ascending aorta with its valve has been used for reconstruction of the right ventricular outflow. This technique has been applied to 123 operations for pulmonary autograft replacement of the aortic valve, 48 opera...

Seven cases of single ventricle, six cases of hypoplasia of the right heart (tricuspid atresia), and one case of hypoplasia of the left heart were investigated with reflected ultrasound. In hypoplasia of the right heart there was abnormal anterior movement of the mitral valve; in hypoplasia of the left heart, abnormal anterior movement of the tricuspid valve, and in single ventricle, similiar m...