Objective. To determine the effects of enzyme replacement therapy (ERT) on the hearing acuity in patients with Fabry disease. Materials. The study sample comprised 34 ears of 17 affected patients who underwent pure-tone audiometry before and after ERT. Methods. The patients were studied in relation to factors such as changes in hearing, presence of accompanying symptoms, status of renal and car...

In 1957 Landau and Kleffner described an unusual childhood disorder which they termed ‘syndrome of acquired aphasia with convulsive disorder’, in which language regresses after a period of normal development and seizures develop. Children with this disorder typically have severe receptive language difficulties and often are at first thought to be deaf. However, pure-tone audiometry shows normal...

Introduction Researchers studying the hearing health of forestry workers have revealed the presence of a noise-induced hearing loss (NIHL) in this population and have concluded that the vibration of the equipment, the carbon monoxide released by motors, and pesticides might also contribute to NIHL. Objective To analyze the noise exposure in the Brazilian forestry industry workers and the effect...

AIMS To characterise the development of noise induced damage to hearing. METHODS Hearing and noise exposure were prospectively monitored among a cohort of newly enrolled construction industry apprentices and a comparison group of graduate students, using standard pure tone audiometry and distortion product otoacoustic emissions (DPOAEs). A total of 328 subjects (632 ears) were monitored annua...

Early intervention through hearing screening can reduce the negative impact of hearing loss for children. Optimal outcomes are achieved when an appropriate screening protocol is selected, a pathway for follow up care is established, and when a hearing conservation component is included. This study aimed to describe the outcomes of a hearing screening service provided to grade one learners in ur...

OBJECTIVES The aim of the study was to determine the characteristics of patients who did not match the audiometric criteria of idiopathic sudden sensorineural hearing loss (SSNHL) but complained of acute hearing loss. METHODS By thorough medical chart reviews, historical cohort study was performed with consecutive data of 589 patients complaining of acute unilateral sensorineural hearing loss...

OBJECTIVES/HYPOTHESIS The present study aimed to examine whether the response patterns to the chimeric lexical tone tokens, combined with their pure tone audiometry (PTA) results, could separate listeners with sensorineural hearing loss (SNHL) from listeners with auditory neuropathy spectrum disorder (ANSD). STUDY DESIGN Case-control study. METHODS Forty-three SNHL subjects and 46 ANSD subj...

PURPOSE To assess the prevalence of tinnitus and possible association with hearing loss, diabetes mellitus and hypertension in elderly. METHODS Cross-sectional study with individuals older than 60 years who underwent audiological evaluation (pure tone audiometry and history) and answered a comorbidity questionnaire. We evaluated 519 subjects of both genders with a median age of 69 years. Indi...

CONTEXT Recently, several studies have investigated the relationship between diabetes and hearing impairment, but results were inconsistent. OBJECTIVE Our objective was to compare the prevalence of hearing impairment between diabetic and nondiabetic adults. DATA SOURCES We performed a systematic literature search using MEDLINE (1950 to May 30, 2011) and EMBASE (1974 to May 30, 2011). STUD...

INTRODUCTION A considerable high number of SNHL patients also suffer from dizziness and related vestibular symptoms. OBJECTIVE To evaluate the association of vestibular dysfunction and sensorineural hearing loss (SNHL) in adult patients. METHODS Prospective, double-blinded, controlled studies composed by 63 adult patients without any vestibular symptoms or diagnosed vestibular diseases. Aud...