endocarditis and intracardiac infection have been increased recently especially in dialysis dependent renal failure patients. this is usually intractable infection to broad spectrum antibiotic therapy and in most cases surgical intervention was necessary. we have presented 45 years old man with intracardiac infection at the tip of dialysis catheter that after catheter removal intracardiac infec...

discussion this is the first iranian 3-oxothiolase deficiency case report as searched in the literature. because of the high rate of consanguineous marriages in iran, physicians should consider the 3-oxothiolase deficiency in the differential diagnosis of any patient with intractable vomiting and severe metabolic acidosis. case presentation this is a case report of 3-oxothiolase deficiency in a...