IdIopAthIc InterstItIAl pneumonIAs The terminology of idiopathic interstitial pneumonias (IIP) varies from country to country and is often confusing. It is called idiopathic pulmonary fibrosis (IPF) in the United States,7 cryptogenic fibrosing alveolitis (CFA) in the United Kingdom8 or idiopathic interstitial pneumonia in Japan.9 In our country, it is termed either as IPF or CFA. The landmark c...

Respiratory bronchiolitis-associated interstitial lung disease (RB-ILD) is a rare, mild inflammatory pulmonary disorder that occurs almost exclusively in current or former heavy smokers, usually between the third and sixth decades, most likely with no gender predilection. The onset is usually insidious with exertional dyspnea and persistent cough, which may be non-productive, developing over a ...

Scleroderma-related interstitial lung disease (SSc-ILD) is a pulmonary fibrosing disorder characterized by systemic inflammation and progressive scarring of the lungs that leads to respiratory failure. Although certain immunosuppressive therapies may slow disease progression, current treatment strategies are not curative; consequently, SSc-ILD continues to be a major cause of morbidity and mort...