BACKGROUND Considered a rare disorder, superficial siderosis of the central nervous system (SSCN) has become more frequently diagnosed in recent years. As it is characterized by progressive sensorineural hearing loss, patients' needs may surpass the capability of hearing aid technology. Despite the retrocochlear nature of the disorder, patients have undergone cochlear implantation (CI) with var...

UNLABELLED Alport Syndrome (AS) is a hereditary disease, characterized by nephropathy, often times with sensorineural hearing loss and ocular defects. AIM to analyze the clinical and hearing information from individuals with AS, more specifically the correlation between renal disorder and hearing loss (HL). STUDY DESIGN clinical prospective with cross-sectional cohort. MATERIALS AND METHO...

Effect of vibration-induced white finger (VWF) on the hearing was examined in 289 Japanese forest workers. From 51 subjects suffering from VWF and 228 with no history of VWF, 37 pairs were formed, matched for age and hours of noise exposure. The cases with VWF had a significantly higher hearing threshold at 4 and 8 kHz than their matched controls. This result was corroborated by the follow-up s...

Perrault syndrome 5 is a rare autosomal recessive disorder that characterized by the association of sensorineural hearing loss and ovarian dysgenesis in females with diversity neurologic deficits due to variants twinkle mtDNA helicase (<i>TWNK</i>) gene. Since develop gradually, patient often misdiagnosed other neurological disease during early age. Herein, we report case geneticall...

BACKGROUND & OBJECTIVES Hearing impairment is a common and heterogeneous sensory disorder in humans. Among about 90 genes, which are known to be associated with hearing impairment, mutations in the GJB2 (gap junction protein beta 2) gene are the most prevalent in individuals with hereditary hearing loss. Contribution of the other deafness-causing genes is relatively poorly understood. Here, we ...

The purpose of this study was to determine if peripheral hearing loss of varying degrees in elderly subjects affected performance on monotic auditory processing disorder (APD) tests. A battery of monotic APD tests was administered to a group of well-educated and high-functioning older adults who were divided into three subgroups based on hearing acuity but similar in age: (1) normal hearing out...

UNLABELLED In newborn hearing screening little importance is attributed to changes in the middle ear. Children with secretory otitis in the neonatal period are at risk for developing otitis media in the first year of life. AIM To determine if children who failed the hearing screening because of conductive hearing loss have more episodes of conductive hearing impairment during their first year...

BACKGROUND Tinnitus is a frequent, debilitating hearing disorder associated with severe emotional and psychological suffering. Although a link between stress and tinnitus has been widely recognized, the empirical evidence is scant. Our aims were to test for dysregulation of the stress-related hypothalamus-pituitary adrenal (HPA) axis in tinnitus and to examine ear sensitivity variations with co...

ABSTRACT Purpose: to analyze the use of a screening tool, by teachers, identify auditory behavior students who are learning read and write. Methods: cross-sectional study including 22 answered Fisher’s Auditory Problems Checklist (QFISHER). The analysis this questionnaire approached categories hearing, attention, memory, language, school performance. chi-square statistical test Mann-Whitney wer...

Sixteen cases of Ramsay Hunt syndrome were investigated concerning the prognosis of facial nerve palsy, hearing impairment, and vestibular disorder. The satisfactory prognosis of facial nerve palsy was achieved in those cases which a good response was evoked by the maximal stimulation test as well as in cases of Bell's palsy. And also, the satisfactory prognosis of hearing impairment was achiev...