INTRODUCTION haemophilia is an inherited bleeding disorder caused by a deficiency in one of the blood coagulation factors. For people affected by severe haemophilia, the deficiency can cause spontaneous internal bleeding. Most young people with severe haemophilia in the UK follow a preventative treatment regimen (prophylaxis) consisting of several intravenous injections of factor concentrate ea...

OBJECTIVE The main objective of this study was to examine factors associated with utilization and costs for persons with haemophilia. STUDY DESIGN Utilization data and patient characteristics were collected through medical record review of 336 patients receiving treatment for at least 90% of their haemophilia care at one of five comprehensive haemophilia treatment centres in California. PRI...

The authors reported the case of a 25-year-old man who complained of pain in the left flank. The sonography exam suspected an abcess more than an hematoma of the left psoas muscle. Urgent surgery did not find the abcess. The biology pointed out a moderate form of haemophilia, Type A. The bedrest and the dressings were efficient on the patient. Follow-up sonography exams revealed a liquefaction ...

Haemophilia A is an inherited, sex-linked disorder in which coagulation factor VIII (FVIII) is deficient or absent [1]. The hallmark of the severe form of the disease, defined as plasma FVIII level of <1% of normal [2], is early, recurrent bleeding into soft tissues and joints [3]. Intra-articular bleeding (haemarthrosis) accounts for more than 90% of all serious bleeding events in patients wit...

Improvements in the management of haemophilia have led to a significant increase in the life expectancy of haemophilia patients, which is now close to the life expectancy in the general male population. Therefore, age-related conditions, especially cardiovascular disease (CVD), have become increasingly common in these patients. The management of CVD, especially that of coronary artery disease (...

BACKGROUND Severe haemophilia is associated with major psychological and economic burden for patients, caregivers, and the wider health care system. This burden has been quantified and documented for a number of European countries in recent years. However, few studies have taken a standardised methodology across multiple countries simultaneously, and sought to amalgamate all three levels of bur...