نتایج جستجو برای: germline mutation

تعداد نتایج: 300136  

Journal: :The British journal of dermatology 1997
C Esche R Kruse C Lamberti W Friedl P Propping P Lehmann T Ruzicka

We report a 62-year-old man with rectal cancer, two keratoacanthomas and multiple sebaceous adenomas, epitheliomas and sebaceous hyperplasia. His brother and father died from colorectal cancer. A subgroup of patients with the Muir-Torre syndrome (MTS) is allelic to the cancer family syndrome. This genetic disorder is caused by an autosomal dominant inherited germline mutation in one of the DNA ...

Journal: :Clinical science 1997
A J Jeffreys

1. Minisatellites, originally developed for forensic DNA fingerprinting and profiling, have also provided extremely informative systems for analysing processes of tandem repeat DNA turnover in the human genome. 2. Minisatellite instability involves distinct mutation processes in somatic and germline cells. In sperm, tandem repeat instability most likely arises at meiosis as a by-product of high...

2016
Nada El Ghorayeb Solange Grunenwald Serge Nolet Vanessa Primeau Stéphanie Côté Christine M. Maugard André Lacroix Louis Gaboury Isabelle Bourdeau

BACKGROUND Adrenocortical carcinoma (ACC) may rarely be a component of inherited cancer syndromes such as Li-Fraumeni syndrome and Beckwith-Wiedemann syndrome. ACC caused by a BRCA2 mutation has never been reported. METHODS Nucleotide sequencing of BRCA2 in lymphocyte and tumoral DNA of a 50-year-old male who presented with an androgen-secreting ACC and a strong family history of breast, ovar...

Journal: :The Journal of Clinical Endocrinology & Metabolism 2007

Journal: :Annals of Surgical Treatment and Research 2014

Journal: :Human molecular genetics 1993
J L Weber C Wong

A total of 20,000 parent-offspring transfers of alleles were examined through the genotyping within 40 CEPH reference families of 28 short tandem repeat polymorphisms (STRPs) located on chromosome 19. Forty-seven initial mutation events were detected in the STRPs using DNA from transformed lymphoblastoid cell lines, but less than half (39%) could be verified using DNA from untransformed cells. ...

Journal: :Journal of medical genetics 2004
E Domingo P Laiho M Ollikainen M Pinto L Wang A J French J Westra T Frebourg E Espín M Armengol R Hamelin H Yamamoto R M W Hofstra R Seruca A Lindblom P Peltomäki S N Thibodeau L A Aaltonen S Schwartz

BACKGROUND According to the international criteria for hereditary non-polyposis colorectal cancer (HNPCC) diagnostics, cancer patients with a family history or early onset of colorectal tumours showing high microsatellite instability (MSI-H) should receive genetic counselling and be offered testing for germline mutations in DNA repair genes, mainly MLH1 and MSH2. Recently, an oncogenic V600E ho...

Journal: :Cancer research 2001
T Liu H Yan S Kuismanen A Percesepe M L Bisgaard M Pedroni P Benatti K W Kinzler B Vogelstein M Ponz de Leon P Peltomäki A Lindblom

Hereditary nonpolyposis colorectal cancer (HNPCC) is attributable to a deficiency of mismatch repair. Inactivation of DNA mismatch repair underlies the genesis of microsatellite instability in colorectal cancer. Germline mutations in three DNA mismatch repair genes, hMSH2, hMLH1, and hMSH6, have been found to segregate in HNPCC and HNPCC-like families. The two DNA mismatch repair genes hPMS1 an...

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