نتایج جستجو برای: cerebellar ataxia

تعداد نتایج: 40653  

Journal: :Neuropediatrics 2012
Maja Steinlin

Acute cerebellitis is thought to be a rare problem in childhood; however, its more benign variant—acute cerebellar ataxia—is the most frequent reason for children presenting in an emergency department for ataxia.1 With increasing use of magnetic resonance imaging in children with acute ataxia, it becomes more and more obvious that there is a continuum of parainfectious reactions of the cerebell...

Journal: :Hong Kong medical journal = Xianggang yi xue za zhi 2003
W L Yeung C K Li E A S Nelson K W Chik G M Joynt E Yuen C K Yeung

Acute cerebellar ataxia and opsomyoclonus are presenting signs of occult neuroblastoma for a substantial proportion of paediatric patients. Cerebellar ataxia may be due to antibodies against the neuroblastoma cross-reacting with cerebellar tissue. This report is of a 26-month-old boy who presented with encephalitis-like features of ataxia, seizures, decreased consciousness, and involuntary move...

Journal: :Journal of Neurology, Neurosurgery & Psychiatry 1999

2012
Jiing-Feng Lirng Po-Shan Wang Hung-Chieh Chen Bing-Wen Soong Wan Yuo Guo Hsiu-Mei Wu Cheng-Yen Chang

PURPOSE A broad spectrum of diseases can manifest cerebellar ataxia. In this study, we investigated whether proton magnetic resonance spectroscopy (MRS) may help differentiate spinocerebellar ataxias (SCA) from multiple systemic atrophy- cerebellar type (MSA-C). MATERIAL AND METHODS This prospective study recruited 156 patients with ataxia, including spinocerebellar ataxia (SCA) types 1, 2, 3...

Journal: :Annals of the New York Academy of Sciences 2005
Caroline Tilikete Alain Vighetto Paul Trouillas Jérome Honnorat

Glutamic acid decarboxylase (GAD) catalyzes the conversion of glutamic acid to gamma-aminobutyric acid (GABA). Autoantibodies directed against GAD (antiGAD-Ab) have been described in patients with insulin-dependent diabetes mellitus, stiff-man syndrome, and in a few patients with progressive cerebellar ataxia. The presence of these autoantibodies suggests an autoimmune pathophysiological mechan...

Journal: :Journal of neurology, neurosurgery, and psychiatry 1995
P Haggard R C Miall D Wade S Fowler A Richardson P Anslow J Stein

The objective was to investigate the anatomical substrate of ataxia seen after severe head injury. Five patients were recruited from present and former inpatients at Rivermead Rehabilitation Centre. All patients had had a closed head injury and all had cerebellar type ataxia. Four normal controls were also studied. Brain MRI, clinical examination, computer based recording, and analysis of visuo...

2005
Cahide Yılmaz Hüseyin Çaksen

Correspondence: Cahide Yılmaz, MD, Yüzüncü Yıl Üniversitesi, Tıp Fakultesi, Çocuk Hastalıkları AD, Van, Türkiye Tel: 904322176128, Fax: 904322150479 E-mail: [email protected] Neurological complications caused by chickenpox are estimated as approximately 0.01%0.03%. Frequent complications related to central nerve system involvement are cerebellar ataxia and encephalitis, and rare complicat...

Journal: :Brain : a journal of neurology 2014
Jérôme Delplanque David Devos Vincent Huin Alexandre Genet Olivier Sand Caroline Moreau Cyril Goizet Perrine Charles Mathieu Anheim Marie Lorraine Monin Luc Buée Alain Destée Guillaume Grolez Christine Delmaire Kathy Dujardin Delphine Dellacherie Alexis Brice Giovanni Stevanin Isabelle Strubi-Vuillaume Alexandra Dürr Bernard Sablonnière

Autosomal dominant cerebellar ataxia corresponds to a clinically and genetically heterogeneous group of neurodegenerative disorders that primarily affect the cerebellum. Here, we report the identification of the causative gene in spinocerebellar ataxia 21, an autosomal-dominant disorder previously mapped to chromosome 7p21.3-p15.1. This ataxia was firstly characterized in a large French family ...

2017
Zheyu Xu Tchoyoson C.C. Lim Wing Lok Au Louis C.S. Tan

Progressive supranuclear palsy (PSP) with predominant cerebellar ataxia (PSP-C) is a rare phenotype of PSP. The clinical and radiological features of this disorder remain poorly characterized. Through a retrospective case series, we aim to characterize the clinical and radiological features of PSP-C. Four patients with PSP-C were identified: patients who presented with prominent cerebellar dysf...

Journal: :Journal of medical genetics 2004
G J Breedveld B van Wetten G D te Raa E Brusse J C van Swieten B A Oostra J A Maat-Kievit

T he cerebellar ataxias are a heterogeneous group of neurodegenerative disorders, characterised by symptoms and signs of cerebellar degeneration, pyramidal and extrapyramidal features, and variable polyneuropathy. Prominent clinical features are signs of cerebellar ataxia, such as uncoordinated gait and uncontrolled co-ordination of hand, speech, and eye movements, while (extra) pyramidal signs...

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