نتایج جستجو برای: cdkl5

تعداد نتایج: 205  

2017
Yimin Wang Xiaonan Du Rao Bin Shanshan Yu Zhezhi Xia Guo Zheng Jianmin Zhong Yunjian Zhang Yong-hui Jiang Yi Wang

Genetic factors play a major role in the etiology of epilepsy disorders. Recent genomics studies using next generation sequencing (NGS) technique have identified a large number of genetic variants including copy number (CNV) and single nucleotide variant (SNV) in a small set of genes from individuals with epilepsy. These discoveries have contributed significantly to evaluate the etiology of epi...

Journal: :Human mutation 2012
Elisa Grillo Laurent Villard Angus Clarke Bruria Ben Zeev Mercedes Pineda Nadia Bahi-Buisson Anna Hryniewiecka-Jaworska Thierry Bienvenu Judith Armstrong Ana Roche-Martinez Francesca Mari Edvige Veneselli Silvia Russo Aglaia Vignoli Giorgio Pini Milena Djuric Anne-Marie Bisgaard Vlatka Mejaški Bošnjak Noémi Polgár Francesca Cogliati Kirstine Ravn Maria Pintaudi Béla Melegh Dana Craiu Aleksandra Djukic Alessandra Renieri

Rett syndrome (RTT) is a neurodevelopmental disorder with one principal phenotype and several distinct, atypical variants (Zappella, early seizure onset and congenital variants). Mutations in MECP2 are found in most cases of classic RTT but at least two additional genes, CDKL5 and FOXG1, can underlie some (usually variant) cases. There is only limited correlation between genotype and phenotype....

2016
Yan Wang Wei Peng Hong-Yan Guo Hui Li Jie Tian Yu-Jing Shi Xiao Yang Yao Yang Wan-Qiao Zhang Xin Liu Guan-Nan Liu Tao Deng Yi-Min Sun Wan-li Xing Jing Cheng Zhi-Chun Feng

Neonatal hypotonia is extremely challenging to diagnose because numerous disorders present similar clinical manifestations. Two panels for diagnosing neonatal hypotonia were developed, which enriches 35 genes corresponding to 61 neonatal hypotonia-related disorders. A cohort of 214 neonates with hypotonia was recruited from 2012 to 2014 in China for this study. Of these subjects, twenty-eight n...

2015
Marta Codina-Solà Benjamín Rodríguez-Santiago Aïda Homs Javier Santoyo Maria Rigau Gemma Aznar-Laín Miguel del Campo Blanca Gener Elisabeth Gabau María Pilar Botella Armand Gutiérrez-Arumí Guillermo Antiñolo Luis Alberto Pérez-Jurado Ivon Cuscó

BACKGROUND Autism spectrum disorders (ASD) are a group of neurodevelopmental disorders with high heritability. Recent findings support a highly heterogeneous and complex genetic etiology including rare de novo and inherited mutations or chromosomal rearrangements as well as double or multiple hits. METHODS We performed whole-exome sequencing (WES) and blood cell transcriptome by RNAseq in a s...

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