The association of arachnodactyly with other skeletal abnormalities and with ocular and cardiac malformations is now well recognized, and numbers of cases illustrating the syndrome have been reported in recent years. The main cardiac malformations have been degeneration of the aortic media with dissecting aneurysm or aneurysmal dilatation, usually of the ascending aorta, but coarctation, change...

Generally coarctation of aorta causes left ventricular dilatation which leads to systolic murmur of mitral regurgitation but in our case of coarctation of aorta the patient had submitral aneurysm as a cause of mitral regurgitation. As such coactation of aorta and submitral aneurysm rarely coexist.

root asymmetry in marfan patients; evaluation by magnetic resonance imaging and comparison with standard echocardiography. Smooth muscle lineage diversity in the chick embryo. Two types of aortic smooth muscle cell differ in growth and receptor-mediated transcriptional responses to transforming growth factor-beta. Comparison of aortic elasticity in patients with the Marfan syndrome with and wit...

The aim of this study was to examine signal intensities of data sets from MR thoracic aortography and to evaluate three-dimensional surface display (3DSD) for postprocessing. Twenty-five patients were imaged with gadolinium-enhanced 3D fast gradient echo sequence. The intensity at the aortic arch was significantly higher than that at the mediastinal fat (p<0.0001). The signal-to-noise ratio was...

Open surgical repair of thoracoabdominal aortic aneurysms has evolved significantly over the last decades thanks to technical improvements, especially in the area of organ protection. However, despite adjunctive strategies, morbidity and mortality rates are still not negligible. Repair of the thoracoabdominal aorta represents a formidable challenge for surgeons, anesthesiologists and patients a...

In this study, we investigated the effect of a specific chymase inhibitor, 2-(5-formylamino-6-oxo-2-phenyl-1,6-dihydropyrimidine-1-yl)-N-[[3,4-dioxo-1-phenyl-7-(2-pyridyloxy)]-2-heptyl]acetamide (NK3201), in the development of abdominal aortic aneurysm in a hamster experimental model. The abdominal aortic aneurysm was induced by application of elastase onto the abdominal aorta in hamster. Each ...

While superficial temporal artery (STA) vasculitis is typically a disease of the elderly, spontaneous STA aneurysm in children is anecdotic and usually caused by a subjacent vasculitis. Since 1948 around 40 cases have been listed in literature and just 6 of them under the age of 18. Three main forms have been classified: juvenile temporal arteritis, typical giant cells arteritis and temporal ar...

Method From 2003 to 2015 a total number of 84 patients, 63 male and 21 female with average age 51.7 years (from 26 to 86 years), underwent hybrid management of complex aortic pathology. Patients were divided in 5 groups: Group 1: Hybrid aortic debranching in 12 pts (for Aortic dissection type B with retrograde arch dissection in 10 patients and Aortic re-dissection type A after surgical treatme...

In a survey of 7,044 necropsies there were 99 cases of aneurysm of the abdominal aorta and 523 cases of peptic ulceration. The incidence of peptic ulceration in the general necropsy population was 7.2% whilst in cases with aneurysm it was 22.6%. There was a significant increase in duodenal ulceration in males with abdominal aortic aneurysms. The possible causes for this increased incidence are ...

Objective: To compare results of dilatation of native coarctation of the aorta with and without stent implantation. Design: Open, observational, non-randomised study. Patients: 54 consecutive adult patients: 32 with balloon angioplasty alone (group 1) and 22 with stent placement (group 2). Interventions: Balloon dilatation from 1995 to 1997; dilatation with Palmaz stent placement from 1997 to 1...