نتایج جستجو برای: alpha 1 antitrypsin

تعداد نتایج: 2882244  

حاجی زاده, محمد رضا, خوشدل, علیرضا, شفیع پور, محمد رضا, شیخ فتح اللهی, محمود, قریشی, آتنا السادات, محمودی, مهدی,

Background and Objectives: Type 1 diabetes (diabetes mellitus) is a disease associated with metabolism. The most common form of type 1 diabetes is its autoimmune type. Alpha-1-antitrypsin (AAT) is a member of the serine protease inhibitors family and its role is to protect tissue degradation by protease. Hence, its defect or deficiency significantly increases the risk of various diseases. This ...

Journal: :Biomedicines 2023

Approximately 50% of all global blindness is caused by cataract in adults aged ≥50 years. The mechanisms the disease are most arguably related to a redox imbalance and inflammation; therefore, aim study was evaluate processes associated with inflammation patients. Twenty-four patients 22–60 years (62.5% females) participated study, 33 controls 28–60 (66.7% females). Venous blood serum subjects ...

2014
Laura Pini Laura Tiberio Narayanan Venkatesan Michela Bezzi Luciano Corda Maurizio Luisetti Ilaria Ferrarotti Mario Malerba David A Lomas Sabina Janciauskiene Enrico Vizzardi Denise Modina Luisa Schiaffonati Claudio Tantucci

BACKGROUND Alpha-1 antitrypsin is the main inhibitor of neutrophil elastase in the lung. Although it is principally synthesized by hepatocytes, alpha-1 antitrypsin is also secreted by bronchial epithelial cells. Gene mutations can lead to alpha-1 antitrypsin deficiency, with the Z variant being the most clinically relevant due to its propensity to polymerize. The ability of bronchial epithelial...

2018
Kenneth R Chapman Joanna Chorostowska-Wynimko A Rembert Koczulla Ilaria Ferrarotti Noel G McElvaney

Alpha 1 antitrypsin deficiency is a hereditary condition characterized by low alpha 1 proteinase inhibitor (also known as alpha 1 antitrypsin [AAT]) serum levels. Reduced levels of AAT allow abnormal degradation of lung tissue, which may ultimately lead to the development of early-onset emphysema. Intravenous infusion of AAT is the only therapeutic option that can be used to maintain levels abo...

Journal: :Protein engineering, design & selection : PEDS 2004
Hana Im Myung-Jeom Ryu Myeong-Hee Yu

Unlike most globular proteins, the native form of serine protease inhibitors (serpins) is strained. Previous studies of human alpha(1)-antitrypsin, a prototype plasma serpin, revealed that various unfavorable interactions, such as overpacking of side chains, buried polar groups and cavities, are the structural basis of the strain. The local strain could be relieved by various stabilizing single...

Journal: :JPMA. The Journal of the Pakistan Medical Association 1981
A Shahid A A Siddiqui S Aziz M Ansari S J Zuberi M A Waqar

Using isoelectric focusing (IEF) and radial immunodiffusion (RID) techniques, serum samples from 100 normal healthy adults and 21 patients with pulmonary emphysema were analysed to identify various alpha 1 antitrypsin phenotypes and the serum concentrations. Ten percent of the patients had low serum values. The normal or most common genetic form, MM, is the predominant phenotype in both control...

Journal: :Journal of clinical pathology 1979
J K Kelly J S Davies A W Jones

Forty-two cases of hepatocellular carcinoma (HCC) were examined for the presence of the inclusions of alpha-1-antitrypsin (AAT), which indicate a carrier state for the Pi Z gene. These were found in the non-neoplastic liver tissue of two cases of HCC and in one of the 98 control livers, a difference that is not statistically significant. Typical globules of AAT deficiency were not found in HCC ...

2015
OF McElvaney L Fee C O’Connor TP Carroll

Background Alpha-1 antitrypsin deficiency (AATD) is a hereditary disorder defined by low plasma levels of alpha-1 antitrypsin (AAT). It is linked primarily with the development of lung, liver and skin disease. The most common abnormal variant of AAT is the ‘Z’ variant. It is the AATD type most associated with the development of liver disease. The aim of this project is to determine the prevalen...

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