نتایج جستجو برای: slc26a4

تعداد نتایج: 451  

Journal: :Arquivos brasileiros de endocrinologia e metabologia 2008
Adriana Lofrano-Porto Gustavo B Barra Paula P Nascimento Patrícia G G Costa Erica C Garcia Rodrigo F Vaz Ana R T Batista Ana C R de Freitas Bruno L B Cherulli Fayez Bahmad Larissa G Figueiredo Francisco A R Neves Luiz Augusto Casulari

Pendred Syndrome (PS) is an autossomal recessive disorder characterized by sensorineural deafness, goiter and iodide organification defect. The hearing loss is associated with inner ear abnormalities, ranging from an isolated enlarged vestibular aqueduct (EVA) to a typical coclear dysplasia. Mutations in the gene that encodes pendrin (SLC26A4), a chloride/iodide transporter, have been shown to ...

Journal: :International Journal of Pediatric Otorhinolaryngology 2008

2015
Ju Yeon Lee Eun Ju Choi Jinu Lee

BACKGROUND Gap junctions (GJs) are intercellular channels through which molecules smaller than 1 kDa can diffuse, and they have been suggested as drug targets. To develop chemical drugs acting on this target, a high-throughput screening (HTS) system for GJ modulators is necessary. RESULTS We designed a new, high-throughput GJ intercellular communication (GJIC) assay. This assay system consist...

Journal: :PloS one 2016
Alexander Y Сhurbanov Tatiana M Karafet Igor V Morozov Valeriia Yu Mikhalskaia Marina V Zytsar Alexander A Bondar Olga L Posukh

Hearing loss (HL) is one of the most common sensorineural disorders and several dozen genes contribute to its pathogenesis. Establishing a genetic diagnosis of HL is of great importance for clinical evaluation of deaf patients and for estimating recurrence risks for their families. Efforts to identify genes responsible for HL have been challenged by high genetic heterogeneity and different ethn...

2015
Yi Jiang Shasha Huang Tao Deng Lihua Wu Juan Chen Dongyang Kang Xiufeng Xu Ruiyu Li Dongyi Han Pu Dai Yong-Gang Yao

In China, approximately 30,000 babies are born with hearing impairment each year. However, the molecular factors causing congenital hearing impairment in the Xiamen area of Fujian province have not been evaluated. To provide accurate genetic testing and counseling in the Xiamen area, we investigated the molecular etiology of non-syndromic deafness in a deaf population from Xiamen. Unrelated stu...

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