Dear Sir, There is considerable evidence suggesting a relation ship between autoimmune diseases and hearing impairment. As a specific entity, autoimmune sensorineural hearing loss (ASHL) has been reported to occur in association with autoimmune diseases such as rheumatoid arthritis (RA). We wanted to draw attention to this relationship by a case with RA presented sudden hearing loss. Our case w...

loss of hearing is a known problem in patients with chronic renal failure, occurring in 40-xo% of cases and being most often of the high frequency sensorineural type. we performed a study on 50 patients with this disease, including 20 who had undergone a successful kidney transplantation. our results show an 80% incidence of hearing loss in these patients and a chance of improvement in at least...

brown-vialetto-van laere syndrome (bvvls) is a rare neurological disorder. we report our finding about four patients clinically and electrophysiologically diagnosed as bvvls and denoted their clinical features with comparison to previous reports. the first symptom was bilateral hearing loss and the onset of other cranial nerves involvement varied between 0-15 years. our patients represented som...

objective: mumps infection is endemic in iran and mumps parotiditis is a common disease in iranian children. there has been a dramatic decrease in the worldwide incidence of mumps since the introduction and use in 1968 of the very effective and inexpensive mumps vaccine. in iran probably due to a higher percentage of unvaccinated young persons material& methods: this descriptive case-series stu...

conclusion we concluded that cmv is the most common cause of intrauterine infection in infants aged less than 6 months as compared to the healthy ones. we prefer, at least in our country, to consider seropositive (cmv-igm) infants suspected of intrauterine infection (less than 6 months) as congenital form. to arrest the natural progression of congenital cmv, we recommend prolonged course of ora...

OBJECTIVE To determine whether chronic suppurative otitis media may cause sensorineural hearing loss. METHODS The files of 121 patients with unilateral chronic suppurative otitis media were reviewed in a retrospective study. Air conduction and bone conduction threshold averages were calculated over the speech frequencies (500 Hz, 1,000 Hz, and 2,000 Hz). Thresholds at 4 kHz were examined sepa...

Hypertrophic pachymeningitis is a progressive disease resulting in a diffuse thickening of dura mater due to inflammation, tumor or autoimmune diseases, but most cases are idiopathic. It is seldom reported to be related to sensorineural hearing loss, but it can cause sensorineural hearing loss which can be potentially reversed through treatment. Here, we report the case of a 54-year-old woman w...

BACKGROUND Epilepsy, ataxia, sensorineural deafness, tubulopathy syndrome is a multi-organ disorder that links to autosomal recessive mutations in the KCNJ10 gene, which encodes for the Kir4.1 potassium channel. It is mostly described in consanguineous, non-European families. CASE REPORT A European male of non-consanguineous birth, with early-onset, static ataxic motor disorder, intellectual ...

BACKGROUND hearing loss during childhood is considered a risk factor for developmental delay. AIM to verify the performance of children diagnosed with mild hearing loss, conductive and sensorineural, in the Sustained Auditory Attention Ability Test (SAAAT). The purpose of the study was to verify if the test is influenced by the presence of hearing impairment. METHOD a clinical study of the ...

INTRODUCTION Sensorineural emergencies (SNE) are rare clinical situations. Few patients consult early explaining subsequent difficulty in having accurate data and management. Three clinical conditions are considered SNE in otolaryngology; they include sudden sensorineural hearing loss (SSHL), Bell's palsy and acute vertigo. There is very little data available on sensorineural emergencies in our...