Two cases of nevoid basal cell carcinoma syndrome were reported with a review of pertinent literature. The first case was a 59-year-old man, whose autopsy was warranted. Signs and symptoms manifested in this case were basal cell carcinoma, generalized multiple nevi, multiple cysts in the jaws and long bones, pits in the palm and sole, frontal and occipital bossing, ossification of the falx cere...

Patient 1 is a 34-year-old man who was referred to us for multiple basal cell carcinoma (BCC) in 2013. He was diagnosed with medullablastoma at age 3 and had his first BCC at age 12 which was surgically excised. Clinicopathological correlation supported Gorlin-Goltz syndrome as a diagnosis, but no further follow up was given. He is under dental follow up since the age of 20 for multiple odontog...

To cite: Campos MA, Varela P, Baptista A, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2016-216073 DESCRIPTION Acanthosis nigricans (AN) can be classified into eight variants, including the benign, obesity associated, syndromic, malignant, acral, unilateral, medication induced and mixed type. Unilateral nevoid AN (UNAN) is an extremely rare form of AN a...