Children with single ventricle anatomy are among the most complicated and challenging patients encountered in pediatric cardiology. Current management involves staged surgical procedures, beginning with neonatal palliation and followed by a bidirectional cavopulmonary anastomosis in infancy and culminating in the Fontan procedure. The Fontan procedure, despite separating the circulation, remain...

OBJECTIVES Increased arterial stiffness is a risk factor of atherosclerosis and cardio-vascular complications. The aim of the study was to determine whether peripheral vascular function might be an early marker of impaired health status in patients with a single ventricle after Fontan procedure. METHODS AND RESULTS Twenty five consecutive adults (11 women and 14 men) aged 24.7 ± 6.2 years aft...

A Fontan procedure has been performed on 29 patients for tricuspid valvular atresia. The age range was 8 months to 33 years (median 10 years), the pulmonary vascular resistance ranged from 1.8-6.1 units . m2 (mean 3.3 units . m2), and the mean pulmonary arterial pressure ranged from 13-45 mm Hg (mean 21 mm Hg). Twenty-nine previous operations had been performed in 23 patients. Fourteen other as...

Background: For more than five decades, the Fontan or Fontan-Kreutzer procedure has been mainstay treatment for congenital heart disease with a single functioning ventricle. Data concerning epidemiological profiles are poor, especially in countries limited resources. Here, we present cases of children complex (CHD) born Kosovo who underwent some forms palliation measuring renal resistive index ...

OBJECTIVE To study the determinants and outcome of arrhythmias after the Fontan type operation. DESIGN Retrospective analysis of data in patients operated on between 1972 and 1986 (follow up 5-19 years (mean 12 years)). PATIENTS All 60 patients undergoing a Fontan type procedure at the National Heart Hospital, London, during the study period (mean age (SD) 12.3 (6.8) years). RESULTS Posto...

Plastic bronchitis is a rare life-threatening complication of Fontan operation. When medical treatment is ineffective in the setting of high systemic venous pressures, Fontan fenestration may be considered to decompress venous pressures and improve cardiac output by creation of the right-to-left shunting. However, transcatheter approach can be difficult in patients with complex venous anatomy. ...

IREAD WITH GREAT INTEREST THE PAPER OF Mainwaring and his colleagues concerning the use of supplementation of triiodothyronine following the modified Fontan procedure. The authors found an evident reduction in levels of triiodothyronine in the blood both during and after cardiopulmonary bypass in patients undergoing the Fontan procedure. We have encountered similar findings in 47 consecutive ch...