نتایج جستجو برای: langerhans histiocytosis

تعداد نتایج: 12631  

2006
Ion Dina Catalin Copaescu Vlad Herlea Fritz Wrba Claudia Iacobescu

Langerhans’cell histiocytosis (Histiocytosis X) is a rare disease of unknown cause characterized by oligoclonal proliferation of Langerhans cells. It occurs mostly in children and young adults and involves one or more body systems such as bone, hypothalamus, posterior pituitary gland, lymph nodes, liver or various soft tissues.The diagnosis is always made by a histological approach.We report a ...

2011
Fu-Chen Chuang Erick Chern Wei-Ming Wu

Progressive nodular histiocytosis is a rare non-Langerhans histiocytosis. It tends to occur in adult with progressive course that differentiates from other groups of xanthogranuloma. The clinical presentation is characteristic and disfiguring of the face is not uncommon. Extracutaneous involvement and metabolic association were reported in a few cases. Treatment is unsatisfactory and follow-up ...

Journal: :Blood 2014
Gayane Badalian-Very

In this issue of Blood, Hervier et al has identified that cooccurrence of Langerhans cell histiocytosis (LCH) and Erdheim-Chester disease (ECD) in the same patient is not a rare event. Mixed histiocytosis (MH) highlights existence of a link between distinct groups of histiocytic disorders and suggests presence of a common progenitor cell. Today, histiocytic disorders are classified into 3 group...

Journal: :Cancer discovery 2016
Eli L Diamond Benjamin H Durham Julien Haroche Zhan Yao Jing Ma Sameer A Parikh Zhaoming Wang John Choi Eunhee Kim Fleur Cohen-Aubart Stanley Chun-Wei Lee Yijun Gao Jean-Baptiste Micol Patrick Campbell Michael P Walsh Brooke Sylvester Igor Dolgalev Olga Aminova Adriana Heguy Paul Zappile Joy Nakitandwe Chezi Ganzel James D Dalton David W Ellison Juvianee Estrada-Veras Mario Lacouture William A Gahl Philip J Stephens Vincent A Miller Jeffrey S Ross Siraj M Ali Samuel R Briggs Omotayo Fasan Jared Block Sebastien Héritier Jean Donadieu David B Solit David M Hyman José Baselga Filip Janku Barry S Taylor Christopher Y Park Zahir Amoura Ahmet Dogan Jean-Francois Emile Neal Rosen Tanja A Gruber Omar Abdel-Wahab

UNLABELLED Histiocytic neoplasms are clonal, hematopoietic disorders characterized by an accumulation of abnormal, monocyte-derived dendritic cells or macrophages in Langerhans cell histiocytosis (LCH) and non-Langerhans cell histiocytosis (non-LCH), respectively. The discovery of BRAF(V600E) mutations in approximately 50% of these patients provided the first molecular therapeutic target in his...

2015
Yeun Seoung Choi Jung Soo Lim Woocheol Kwon Soon-Hee Jung Il Hwan Park Myoung Kyu Lee Won Yeon Lee Suk Joong Yong Seok Jeong Lee Ye-Ryung Jung Jiwon Choi Ji Sun Choi Joon Taek Jeong Jin Sae Yoo Sang-Ha Kim

Pulmonary Langerhans cell histiocytosis is an uncommon diffuse cystic lung disease in adults. In rare cases, it can involve extrapulmonary organs and lead to endocrine abnormalities such as central diabetes insipidus. A 42-year-old man presented with polyphagia and polydipsia, as well as a dry cough and dyspnea on exertion. Magnetic resonance imaging of the hypothalamic-pituitary system failed ...

Journal: :International Journal of Research in Medical Sciences 2020

Journal: :The Journal of bone and joint surgery. American volume 1996
S E Levine J P Dormans J S Meyer T A Corcoran

Between May 1972 and December 1991, 58 children were seen in the authors' institution for treatment of Langerhans' cell histiocytosis. Of these, 15 children (7 males, 8 females) had biopsy-proven Langerhans' cell histiocytosis with vertebral involvement. The average age at presentation was 6.4 years (range, 0.2-13.3 years). At presentation, 8 patients had involvement of a single vertebra and 4 ...

2016
Jimyung Seo Howard Chu Jin Sung Lee Do Young Kim

264 Ann Dermatol Received February 24, 2015, Revised May 7, 2015, Accepted for publication May 7, 2015 Corresponding author: Do Young Kim, Department of Dermatology, Severance Hospital, Cutaneous Biology Research Institute, Yonsei University College of Medicine, 50 Yonsei-ro, Seodaemoon-gu, Seoul 03722, Korea. Tel: 82-2-2228-2080, Fax: 82-2-393-9157, E-mail: [email protected]. This is an Open Acces...

Journal: :Journal of gastrointestinal and liver diseases : JGLD 2017
George P Christophi Yeshika Sharma Quader Farhan Umang Jain Ted Walker Gregory S Sayuk Deborah C Rubin

BACKGROUND Non-Langerhans histiocytosis is a group of inflammatory lymphoproliferative disorders originating from non-clonal expansion of hematopoietic stem cells into cytokine-secreting dendritic cells or macrophages. Erdheim-Chester Disease (ECD) is a rare type of non-Langerhans cell histiocytosis characterized by tissue inflammation and injury caused by macrophage infiltration and histologic...

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