cor triatriatum is defined as a membrane within the left atrium, which might lead to restricted pulmonary venous return. diagnosis is usually achieved by echocardiography in early infancy. therapy of choice is the excision of the membrane. herein, successful correction of cor triatriatum in a 4-year-old girl is presented, and the clinical features, echocardiographic findings, and the surgical t...

pulmonary arterial hypertension (pha) is a frequent complication of congenital heart disease (chd), most commonly in systemic-to-pulmonary shunt lesions. in patients with an uncorrected left-to right shunt, pah will end up to eisenmenger’s syndrome, which is contraindication of surgery. what about patients with moderate to severe pah, who do not have criteria of eisenmenger’s syndrome; immediat...

conclusions no significant difference in reducing post bypass inflammation between preoperative steroid treatment and combined preoperative and intraoperative steroid administration reported and they had the same effects. results in both groups, no significant difference with variation of expression for il-6 (inflammatory factor) and il-10 (anti-inflammatory factor) in different times after byp...

background oral cleft is the most common orofacial congenital anomaly among live births. this anomaly at birth is one of the main causes of children disability and mortality.  congenital heart disease (chd) is one of the most common anomalies in oral clefts.  this study aimed to assess the incidence of congenital heart diseases anomalies in newborns with oral clefts. materials and methods this ...

conclusions there was no difference in clinical outcome after cardiac surgery when we administered an additional dose of methylprednisolone compared to a single dose of methylprednisolone. patients and methods sixty pediatric patients (age < 5years) undergoing cardiopulmonary bypass surgery between september 2011-2012 at imam reza hospital-mashhad were randomly assigned to receive preoperative ...

the relationship between congenital heart disease (chd) and growth retardation is well documented. we investigated the growth condition of iranian children with several types of congenital heart disease (chd) and compared it with worldwide researches. growth condition was investigated in 469 patients with important chd aged from 1 month to 18 years. the patients were divided into two groups; in...

Apart from complete and incomplete congenital heart block (CHB), new cardiac manifestations related to anti-SSA/Ro antibodies have been reported in children born to mothers bearing these antibodies. These manifestations include transient fetal first-degree heart block, prolongation of corrected QT (QTc) interval, sinus bradycardia, late-onset cardiomyopathy, endocardial fibroelastosis and cardi...

OBJECTIVE This prospective study aimed to identify antibody profiles characterising mothers with fetuses developing congenital heart block (CHB) by comparing their antibody frequencies and levels with those in unaffected mothers. METHODS Eighty-one consecutive pregnant patients positive to anti-Ro±anti-La antibodies, at high risk of developing fetal CHB were prospectively studied. The 16 pati...

A 48-year-old female presented with complete heart block. On evaluation, it was diagnosed as a congenital cyanotic heart disease, namely, L-transposition of great arteries (L-TGA) with Fallot's physiology. She led the normal life of a manual laborer and had three hospital deliveries and yet escaped detection of her cardiac condition.

FAMILIAL COMPLETE HEART BLOCK (CHB) has been described by a number of observers since the report by Morquio' in 1901. Among those reported are thirteen families with multiple cases of well-documented congenital CHB2-14 using the classic criteria of Yater'5 and eliminating those with intracardiac defects. More recently, an association has been noted between congenital CHB and maternal connective...