Amelogenesis imperfecta (AI) remains a poorly understood group of hereditary enamel defects characterized by a wide array of clinical presentations. Although numerous reports have described the histological features of AI, knowledge concerning the biochemical composition of the affected enamel remains minimal. The purpose of this investigation was to examine the protein of smooth hypoplastic AI...

Amelogenesis Imperfectas (AIs) are clinically and genetically heterogeneous conditions characterized by a wide range of clinical features. These abnormalities of enamel formation are categorized into three main groups, hypoplastic, hypomaturation and hypocalcified with different modes of inheritance such as autosomal recessive (AR), autosomal dominant (AD) and X-lined recessive (XLR). In spite ...

Two rare cases of asymmetrical tooth destruction affecting the primary dentition and 1 case of hypoplastic, vertical striping X-linked amelogenesis imperfecta which affects the permanent dentition in an asymmetrical manner, are presented. The etiology of the conditions are discussed with respect to inheritance, preeruptive and posteruptive influences. The asymmetrical gross tooth destruction re...