A 9-year old boy had severe muscle weakness and typical skin rash and EMG with diagnosis of dermatomyositis associated with erythrodermia with islands of normal skin and palmoplantar hyperkeratosis, which was reported. As PRP in skin biopsy. Association dermatomyositis with PRP is very rare.

Pityriasis rubra pilaris (PRP) represents a group of rare inflammatory skin disorders. Diagnosis is often challenging, its treatment mainly empirical and suffers from the lack controlled trials. PRP shares overlapping clinical histological features with psoriasis, suggesting common underlying pathophysiology. Based on this resemblance, role IL23–TH17-axis in was proposed, several cases successf...